Abstract
NIV is used routinely in patients with cystic fibrosis despite the evidence in the literature supporting this practice being fairly limited. The main indications to use NIV in CF are airway clearance, hypoxaemia, acute and chronic ventilatory failure.
This short review will summarise the rationale for using NIV in patients with cystic fibrosis in these settings.
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Abbreviations
- ABG:
-
Arterial blood gas
- AHI:
-
Apnoea hypopnoea index
- CF:
-
Cystic fibrosis
- CPT:
-
Chest physiotherapy
- FEV1:
-
Forced expiratory volume in 1 s
- FiO2:
-
Fraction of inspired oxygen
- IMV:
-
Invasive mechanical ventilation
- IV:
-
Intravenous
- MDT :
-
Multidisciplinary team
- NIV :
-
Non-invasive ventilation
- ODI:
-
Oxygen desaturation index
- tcCO2:
-
Transcutaneous CO2
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Spoletini, G. (2022). Non-invasive Ventilation in Adults with Cystic Fibrosis. In: Esquinas, A.M. (eds) Teaching Pearls in Noninvasive Mechanical Ventilation. Springer, Cham. https://doi.org/10.1007/978-3-030-71298-3_46
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DOI: https://doi.org/10.1007/978-3-030-71298-3_46
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