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Aneurysmal Bone Cyst and Ewing Sarcoma of the Orbit

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Atlas of Orbital Imaging

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Abstract

Aneurysmal Bone Cyst (ABC)

  • Nonneoplastic, reactive, multicystic and expansile lesion of the orbit.

  • May follow trauma or arteriovenous anomalies of the bone cortex.

  • Orbital roof is most commonly involved.

  • CT scans show a multiloculated expansile, interdiploic lesion with cortical remodeling.

  • Peripheral capsule and internal septations of the lesion are usually enhanced.

  • MRI usually depicts a multiloculated isointense lesion on SE/T1, with areas of hyperintensity and high signal intensity on T2-weighted imaging. Fluid levels with heterogeneous signal intensities are the classic appearance, depending upon the state of the included blood.

  • Some parts of the lesion may appear densely enhanced with contrast media.

Ewing Sarcoma

  • Poorly circumscribed, heterogeneous lesion typically originating from bony wall of the orbit, most commonly the roof

  • Osteolytic with mottled “moth-eaten” appearance due to erosion and destruction of bone [1]

  • Associated soft tissue component may be present

  • Patchy hypodense areas can indicate old hemorrhage and necrosis [2]

  • Hypo- to isointense on T1-weighted MR imaging

  • Heterogeneously high signal on T2-weighted imaging

  • Heterogeneously contrast-enhancing on CT/MR imaging

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References

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Author information

Authors and Affiliations

  1. Division of Orbital and Ophthalmic Plastic Surgery, Stein Eye Institute, University of California, Los Angeles, CA, USA

    Liza M. Cohen

  2. Division of Orbital and Ophthalmic Plastic Surgery, Stein and Doheny Eye Institutes, University of California, Los Angeles, CA, USA

    Stefania B. Diniz & Robert A. Goldberg

Authors
  1. Stefania B. Diniz
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  2. Liza M. Cohen
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  3. Robert A. Goldberg
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Corresponding author

Correspondence to Robert A. Goldberg .

Editor information

Editors and Affiliations

  1. Ophthalmic Plastic and Lacrimal Surgery Institute, Department of Ophthalmology, The Goldschleger Eye Institute, Sheba Medical Center, Tel Hashomer, Israel

    Guy Ben Simon

  2. Department of Diagnostic Imaging, Sheba Medical Center, Tel Hashomer, Israel

    Gahl Greenberg

  3. Ophthalmic Plastic and Lacrimal Surgery Institute, Department of Ophthalmology, The Goldschleger Eye Institute, Sheba Medical Center, Tel Hashomer, Israel

    Daphna Landau Prat

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Diniz, S.B., Cohen, L.M., Goldberg, R.A. (2022). Aneurysmal Bone Cyst and Ewing Sarcoma of the Orbit. In: Ben Simon, G., Greenberg, G., Landau Prat, D. (eds) Atlas of Orbital Imaging . Springer, Cham. https://doi.org/10.1007/978-3-030-62426-2_48

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  • DOI: https://doi.org/10.1007/978-3-030-62426-2_48

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-62425-5

  • Online ISBN: 978-3-030-62426-2

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