Abstract
Desmoplastic small round cell tumor is a high-grade malignancy of uncertain differentiation. It is also known as intra-abdominal desmoplastic round cell tumor and polyphenotypic small round cell tumor.
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Notes
- 1.
EMA: epithelial membrane antigen.
- 2.
NSE: neuron-specific enolase.
- 3.
WT1: Wilms tumor 1.
- 4.
Pazopanib: tyrosine kinase inhibitor targeting the following: VEGFR, PDGFR, KIT.
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Mocellin, S. (2021). Desmoplastic Small Round Cell Tumor. In: Soft Tissue Tumors . Springer, Cham. https://doi.org/10.1007/978-3-030-58710-9_71
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DOI: https://doi.org/10.1007/978-3-030-58710-9_71
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