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Indolent Cutaneous T-Cell Lymphomas

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Indolent Lymphomas

Part of the book series: Hematologic Malignancies ((HEMATOLOGIC))

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Abstract

Primary cutaneous lymphomas are a heterogeneous group of non-Hodgkin lymphomas that present in the skin with no evidence of extracutaneous disease at the time of diagnosis. Within this group, the majority is derived from T-cells. The different types of cutaneous lymphomas are defined by various clinical manifestations, histological patterns, and immunophenotypic markers. In contrast to the nodal non-Hodgkin lymphomas, primary cutaneous T-cell lymphomas (CTCL) usually represent an indolent disease group and therefore require mostly skin-directed therapies. However, at later stages, certain subtypes run a more aggressive course.

This chapter provides an overview of the most common, indolent CTCL subtypes and summarizes stage-adapted diagnostics and treatment.

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Author information

Authors and Affiliations

  1. Department of Dermatology, Leiden University Medical Centre, Leiden, The Netherlands

    Rein Willemze

  2. Department of Medicine III, LMU Hospital, Munich, Germany

    Sebastian Theurich

  3. Department of Dermatology and Allergology, LMU Hospital, Munich, Germany

    Max Schlaak

Authors
  1. Rein Willemze
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  2. Sebastian Theurich
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  3. Max Schlaak
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Editors and Affiliations

  1. Department of Medicine III, LMU Hospital, München, Bayern, Germany

    Martin Dreyling

  2. Azienda Ospedaliera Nazionale SS Antonio e Biagio e Cesare Arrigo, Alessandria, Italy

    Marco Ladetto

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Willemze, R., Theurich, S., Schlaak, M. (2021). Indolent Cutaneous T-Cell Lymphomas. In: Dreyling, M., Ladetto, M. (eds) Indolent Lymphomas . Hematologic Malignancies. Springer, Cham. https://doi.org/10.1007/978-3-030-55989-2_14

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