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Hypothalamic Neuroendocrine Neoplasms

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The Spectrum of Neuroendocrine Neoplasia

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Abstract

The hypothalamus is now recognized to be the location where signals from the internal milieu and external stimuli are integrated to regulate endocrine homeostasis. Neuroendocrine tumors that arise from neurons in and around the hypothalamus give rise to clinical manifestations of mass effect as well as hormonal activity. These rare tumors include gangliocytomas and neurocytomas that produce hormones and are associated with endocrinopathies.

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Author information

Authors and Affiliations

  1. Department of Pathology, University Hospitals Cleveland Medical Center and Case Western Reserve University, Cleveland, OH, USA

    Sylvia L. Asa

  2. Department of Pathology, University Health Network, Toronto, ON, Canada

    Sylvia L. Asa & Ozgur Mete

  3. Department of Laboratory Medicine and Pathobiology, University of Toronto, Toronto, ON, Canada

    Ozgur Mete

  4. Endocrine Oncology Site, Princess Margaret Cancer Centre, Toronto, ON, Canada

    Ozgur Mete

Authors
  1. Sylvia L. Asa
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  2. Ozgur Mete
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Correspondence to Ozgur Mete .

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Editors and Affiliations

  1. University Hospitals Cleveland Medical Center, Case Western Reserve University, Cleveland, OH, USA

    Sylvia L. Asa

  2. Institute of Pathology, University Hospital of Lausanne, Lausanne, Vaud, Switzerland

    Stefano La Rosa

  3. Department of Pathology, University Health Network, Toronto, ON, Canada

    Ozgur Mete

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Asa, S.L., Mete, O. (2021). Hypothalamic Neuroendocrine Neoplasms. In: Asa, S.L., La Rosa, S., Mete, O. (eds) The Spectrum of Neuroendocrine Neoplasia. Springer, Cham. https://doi.org/10.1007/978-3-030-54391-4_5

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  • DOI: https://doi.org/10.1007/978-3-030-54391-4_5

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