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Atrioventricular Septal Defects

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Pediatric Cardiology

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Abstract

Atrioventricular septal defect is a lesion affecting the atrioventricular junction. Even though all lesions within this group have the same phenotypic anatomy in terms of the common atrioventricular junction, clinical manifestation and surgical approach vary according to the presence or absence of shunting at the ventricular level and presence and extent of atrioventricular valve regurgitation. This chapter reviews the morphological features, clinical presentation, and management of the most commonly encountered clinical scenarios of this lesion, as well as those associated with other congenital heart defects.

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Author information

Authors and Affiliations

  1. Department of Pediatric Cardiology, Leiden University Medical Center (LUMC), Leiden, The Netherlands

    Regina Bökenkamp & Nathan D. Hahurij

Authors
  1. Regina Bökenkamp
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  2. Nathan D. Hahurij
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Correspondence to Regina Bökenkamp .

Editor information

Editors and Affiliations

  1. Lurie Children's Hospital, Northwestern Memorial Hospital, Chicago, IL, USA

    Ra-id Abdulla

  2. Lurie Children's Hospital of Chicago, Northwestern Memorial Hospital, Chicago, USA

    Stuart Berger

  3. Lurie Children's Hospital of Chicago, Northwestern Memorial Hospital, Chicago, USA

    Carl Backer

  4. King's College, University College London, London, UK

    Robert Anderson

  5. Weill Cornell Medical College, Cornell University, New York, USA

    Ralf Holzer

  6. University of Amsterdam, Amsterdam, Noord-Holland, The Netherlands

    Nico Blom

  7. Lurie Children's Hospital of Chicago, Northwestern Memorial Hospital, Chicago, IL, USA

    Joshua Robinson

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Bökenkamp, R., Hahurij, N.D. (2023). Atrioventricular Septal Defects. In: Abdulla, Ri., et al. Pediatric Cardiology. Springer, Cham. https://doi.org/10.1007/978-3-030-42937-9_52-1

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  • DOI: https://doi.org/10.1007/978-3-030-42937-9_52-1

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  • Print ISBN: 978-3-030-42937-9

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