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Cystic Diseases of the Kidney

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Pediatric Surgery

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Abstract

Cystic diseases of the kidney range from indolent, incidentally diagnosed simple renal cysts to severe life-threatening renal insufficiency seen in neonates and infants with autosomal recessive polycystic kidney disease (ARPKD). Multicystic dysplastic kidney (MCDK) and autosomal dominant cystic disease (ADPKD) are examples of the most common cystic kidney diseases seen in clinical practice. This chapter provides a practical overview of the investigation and management for the most common cystic kidney diseases taking into account possible limitations encountered in low-resource settings.

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Author information

Authors and Affiliations

  1. Dalhousie University, Halifax, NS, Canada

    Rodrigo L. P. Romao

  2. Mbarara Univeristy, Mbarara, Uganda

    Martin Situma

  3. The University of Benign Teaching Hospital, Benin City, Nigeria

    Osarumwense David Osifo

  4. Department of Pediatric Surgery, Oxford Children’s Hospital, Oxford, United Kingdom

    Edward Hannon

Authors
  1. Rodrigo L. P. Romao
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  2. Martin Situma
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  3. Osarumwense David Osifo
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  4. Edward Hannon
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Editor information

Editors and Affiliations

  1. Division of Pediatric Surgery, Department of Surgery, National Hospital, Abuja, Nigeria

    Emmanuel A. Ameh

  2. Professor of Surgery & Pediatrics, Rady Children’s Hospital, University of California San Diego, San Diego, CA, USA

    Stephen W. Bickler

  3. Department of Pediatric Surgery, University of Oxford, Oxford, UK

    Kokila Lakhoo

  4. Department of Pediatric Surgery, Nationwide Children’s Hospital, and Department of Surgery, Ohio State University, Colombus, OH, USA

    Benedict C. Nwomeh

  5. Department of Pediatric Surgery, Montreal Children’s Hospital, Montreal, QC, Canada

    Dan Poenaru

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Romao, R.L.P., Situma, M., Osifo, O.D., Hannon, E. (2020). Cystic Diseases of the Kidney. In: Ameh, E.A., Bickler, S.W., Lakhoo, K., Nwomeh, B.C., Poenaru, D. (eds) Pediatric Surgery. Springer, Cham. https://doi.org/10.1007/978-3-030-41724-6_88

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  • DOI: https://doi.org/10.1007/978-3-030-41724-6_88

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-41723-9

  • Online ISBN: 978-3-030-41724-6

  • eBook Packages: MedicineMedicine (R0)

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