Abstract
Erdheim-Chester disease, or lipid granulomatosis, is a rare disorder characterized by the proliferation of histiocytes in bone and in extraosseous locations. It is thought perhaps to be a lipid storage disease, in which foamy lipid-laden histiocytes accumulate in the bone marrow. Extravasated lipid results in cholesterol granulomas and a fibroinflammatory reaction.
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McCarthy, E. (2020). Erdheim-Chester Disease. In: Santini-Araujo, E., Kalil, R.K., Bertoni, F., Park, YK. (eds) Tumors and Tumor-Like Lesions of Bone. Springer, Cham. https://doi.org/10.1007/978-3-030-28315-5_75
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DOI: https://doi.org/10.1007/978-3-030-28315-5_75
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