Abstract
Congenital lung and chest cage malformations encompass a wide range of diseases caused during the development of the lung and rib cage structures. These anomalies are manifested in different ways, depending on when they are originated and at what level they affect the tracheobronchial path. The concept of congenital lung and chest cage considers lesions of the lung parenchyma: cystic adenomatoid malformation, lung sequestration, and congenital lobar emphysema, along other less common lesions: intestinal duplication and bronchogenic cyst. Antenatal diagnosis is common because of the routine obstetric ultrasound, and therefore many authors have proposed the name of genetic malformations, which would be appropriate. Also, the finding of asymptomatic lesions in infants and children is not infrequent. There is a consensus for surgery repair in patients with symptoms secondary to a congenital malformation. However, in asymptomatic patients, management will depend on location, type of lesions, and risk for surgery.
This is a preview of subscription content, log in via an institution to check access.
Access this chapter
Tax calculation will be finalised at checkout
Purchases are for personal use only
Sources
Azizkhan RG, Crombleholme TM. Congenital cystic lung disease: contemporary antenatal and postnatal management. Pediatr Surg Int. 2008;24(6):643–57.
Chen HW, Hsu WM, Lu FL, Chen PC, Jeng SF, Peng SS, Chen CY, Chou HC, Tsao PN, Hsieh WS. Management of congenital cystic adenomatoid malformation and bronchopulmonary sequestration in newborns. Pediatr Neonatol. 2010;51(3):172–7.
Davenport M, Warne SA, Cacciaguerra S, Patel S, Greenough A, Nicolaides K. Current outcome of antenally diagnosed cystic lung disease. J Pediatr Surg. 2004;39(4):549–56.
Kotecha S, Barbato A, Bush A, Claus F, Davenport M, Delacourt C, Deprest J, Eber E, Frenckner B, Greenough A, Nicholson AG, Antón-Pacheco JL, Midulla F. Antenatal and postnatal management of congenital cystic adenomatoid malformation. Paediatr Respir Rev. 2012;13(3):162–70.
Laberge JM, Puligandla P, Flageole H. Asymptomatic congenital lung malformations. Semin Pediatr Surg. 2005;14(1):16–33.
Stocker JT. Cystic lung disease in infants and children. Fetal Pediatr Pathol. 2009;28(4):155–84. Available in https://www.tandfonline.com/doi/full/10.1080/15513810902984095.
Author information
Authors and Affiliations
Corresponding author
Editor information
Editors and Affiliations
Rights and permissions
Copyright information
© 2020 Springer Nature Switzerland AG
About this chapter
Cite this chapter
Pattillo Silva, J.C., Zúñiga Rocha, S., Vuletin Solís, J. (2020). Congenital Lung Malformations. In: Bertrand, P., Sánchez, I. (eds) Pediatric Respiratory Diseases. Springer, Cham. https://doi.org/10.1007/978-3-030-26961-6_54
Download citation
DOI: https://doi.org/10.1007/978-3-030-26961-6_54
Published:
Publisher Name: Springer, Cham
Print ISBN: 978-3-030-26960-9
Online ISBN: 978-3-030-26961-6
eBook Packages: MedicineMedicine (R0)