Abstract
To assess respiratory function in patients with neuromuscular diseases is a challenge because the patient can provide only limited cooperation with the tests and experiences early fatigue when performing repeated maneuvers. This highlights the importance of a well-trained technician to be able to determine if a poor maneuver is acceptable for a given patient. Several tests assess respiratory muscle function, but most of those used are static pressures: the maximum inspiratory pressure, maximum expiratory pressure, and maximum expiratory flow generated by a cough (peak cough flow). A simple but functional test is the walk test, which is related to the actual quality of life.
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Caussade Larraín, S. (2020). Assessment of Respiratory Muscular Function in Patients with Neuromuscular Diseases. In: Bertrand, P., Sánchez, I. (eds) Pediatric Respiratory Diseases. Springer, Cham. https://doi.org/10.1007/978-3-030-26961-6_10
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DOI: https://doi.org/10.1007/978-3-030-26961-6_10
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