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Aortopulmonary Window

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Critical Care of Children with Heart Disease

Abstract

Aortopulmonary (AP) window is a rare cardiac anomaly accounting for 0.1–0.2% of all cases of congenital heart disease. It represents a communication between the ascending aorta and the main pulmonary artery in the presence of two separate semi-lunar valves. While it can occur as an isolated lesion, it is frequently associated with other cardiac defects, including type A interruption of the aortic arch, aortic origin of the right pulmonary artery, Tetralogy of Fallot, anomalous origin of the coronary arteries from the pulmonary artery, transposition of the great arteries, or tricuspid atresia. Pathophysiology of AP window is similar to that of other left-to-right shunt lesions, such as ventricular septal defect (VSD) or patent ductus arteriosus (PDA). AP windows do not close spontaneously, nor do they show decrease in size over time. Therefore, early recognition is important to allow for surgical closure before the development of pulmonary vascular obstructive disease, especially when the defect size is large.

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Correspondence to Wonshill Koh .

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Koh, W., Morell, E., Moguillansky, D., Munoz, R.A., Morell, V.O. (2020). Aortopulmonary Window. In: Munoz, R., Morell, V., da Cruz, E., Vetterly, C., da Silva, J. (eds) Critical Care of Children with Heart Disease . Springer, Cham. https://doi.org/10.1007/978-3-030-21870-6_17

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  • DOI: https://doi.org/10.1007/978-3-030-21870-6_17

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-21869-0

  • Online ISBN: 978-3-030-21870-6

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