Abstract
Netherton syndrome is a rare autosomal recessive disorder presenting with a generalized ichthyosiform erythroderma, characteristic hair shaft abnormality and allergic manifestations
Netherton syndrome is caused by germline mutations in the SPINK5 gene
Management of Netherton syndrome should be multidisciplinary, involving fluid and electrolyte correction, conscientious skin care with frequent application of emollients, prompt treatment of cutaneous and systemic infective complications, and nutritional support
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Lim, Z.V., Gan, E.Y. (2019). Red Peeling. In: Rezaei, N. (eds) Pediatric Immunology. Springer, Cham. https://doi.org/10.1007/978-3-030-21262-9_142
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DOI: https://doi.org/10.1007/978-3-030-21262-9_142
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