Abstract
Non-classifiable periodic fever syndromes are common
Patients may have recurrent fevers or continuous chronic inflammation, together with different combinations of arthralgia/arthritis, mouth ulcers, lymphadenopathies, conjunctivitis, rashes, pleuritic pain, splenomegaly, hepatomegaly and abdominal pain
Inheritance varies from no apparent pattern to autosomal dominant inheritance
Many patients respond to colchicine as a reasonable first-line treatment
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Wekell, P., Fasth, A., Berg, S. (2019). Irregular Recurrent Fever. In: Rezaei, N. (eds) Pediatric Immunology. Springer, Cham. https://doi.org/10.1007/978-3-030-21262-9_113
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DOI: https://doi.org/10.1007/978-3-030-21262-9_113
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