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Ventilator Support in Children with Neuromuscular Disorders

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Caring for the Ventilator Dependent Child

Part of the book series: Respiratory Medicine ((RM))

Abstract

Children with neuromuscular disorders can develop respiratory complications such as respiratory failure, recurrent pulmonary infections and secretion clearance difficulties related to weakness of inspiratory and expiratory muscles, swallowing problems and chest wall disorders. It is increasingly possible to identify children at risk of these problems, monitor their progress and intervene with targeted measures such as non-invasive ventilation and cough assist techniques. These have, in many groups, resulted in improved survival, reduced hospitalisations and enhanced quality of life. In other groups, non-invasive ventilation may be used to palliate symptoms and facilitate discharge to home. Prognosis in Duchenne muscular dystrophy has improved so that these individuals typically live into their late twenties/early thirties and some to middle age, and children with neuromuscular disorders who were previously expected to die in the paediatric age range are now successfully transitioning to adult care. This has important implications for decision-making, service planning, adult pulmonary teams and the patient and family.

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Authors and Affiliations

  1. NIHR Respiratory Biomedical Research Unit, Royal Brompton & Harefield NHS Foundation Trust, Sydney Street, London, SW3 6NP, UK

    Anita K. Simonds M.D., F.R.C.P.

Authors
  1. Anita K. Simonds M.D., F.R.C.P.
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Correspondence to Anita K. Simonds M.D., F.R.C.P. .

Editor information

Editors and Affiliations

  1. Eudowood Division of Pediatric Respiratory Sciences, The Johns Hopkins University School of Medicine, BALTIMORE, Maryland, USA

    Laura M. Sterni

  2. Division of Pediatric Pulmonary and Sleep Medicine, University of Arkansas for Medical Sciences, Little Rock, Arkansas, USA

    John L. Carroll

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Simonds, A.K. (2016). Ventilator Support in Children with Neuromuscular Disorders. In: Sterni, L., Carroll, J. (eds) Caring for the Ventilator Dependent Child. Respiratory Medicine. Humana Press, New York, NY. https://doi.org/10.1007/978-1-4939-3749-3_14

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  • DOI: https://doi.org/10.1007/978-1-4939-3749-3_14

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  • Publisher Name: Humana Press, New York, NY

  • Print ISBN: 978-1-4939-3747-9

  • Online ISBN: 978-1-4939-3749-3

  • eBook Packages: MedicineMedicine (R0)

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