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Pulmonary Hypertension in Congenital Heart Disease

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Cardiac CT and MR for Adult Congenital Heart Disease

Abstract

The occurrence of pulmonary hypertension (PH) in patients with congenital heart disease (CHD) is not uncommon and represents an important complication. This chapter sets out the scale of the problem before describing where cross-sectional imaging is used in diagnosis. Prognostication and assessment of therapeutic effect using these techniques is then explored before examining Eisenmenger’s syndrome in detail. A discussion on related abnormalities of the pulmonary arteries is included.

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Acknowledgments

William Bradlow and Sonya Babu-Narayan have been or continue to be supported by the British Heart Foundation. This work was supported by the NIHR Cardiovascular Biomedical Research Unit of Royal Brompton & Harefield NHS Foundation Trust and Imperial College London. This report is independent research by the National Institute for Health Research Biomedical Research Unit Funding Scheme. The views expressed in this publication are those of the authors and not necessarily those of the NHS, the National Institute for Health Research or the Department of Health.

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Authors and Affiliations

  1. Department of Cardiology, Queen Elizabeth Hospital Birmingham NHS Foundation Trust, Queen Elizabeth Medical Centre, Edgbaston, Birmingham, B15 2TH, UK

    William M. Bradlow BMBS, MRCP, PhD

  2. NIHR Cardiovascular Biomedical Research Unit, Royal Brompton Hospital and National Heart and Lung Institute, Imperial College London, Sydney Street, London, SW3 6NP, UK

    Sonya V. Babu-Narayan MBBS, BSc, MRCP, PhD & Raad H. Mohiaddin MD, FRCR, FRCP, FESC, PhD

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  1. William M. Bradlow BMBS, MRCP, PhD
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  2. Sonya V. Babu-Narayan MBBS, BSc, MRCP, PhD
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  3. Raad H. Mohiaddin MD, FRCR, FRCP, FESC, PhD
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Corresponding author

Correspondence to Sonya V. Babu-Narayan MBBS, BSc, MRCP, PhD .

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  1. Department of Radiology, USC University Hospital Keck School of Medicine, Los Angeles, California, USA

    Farhood Saremi

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Bradlow, W.M., Babu-Narayan, S.V., Mohiaddin, R.H. (2014). Pulmonary Hypertension in Congenital Heart Disease. In: Saremi, F. (eds) Cardiac CT and MR for Adult Congenital Heart Disease. Springer, New York, NY. https://doi.org/10.1007/978-1-4614-8875-0_25

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  • DOI: https://doi.org/10.1007/978-1-4614-8875-0_25

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