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Aortic Arch Anomalies

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Cardiac CT and MR for Adult Congenital Heart Disease

Abstract

Congenital anomalies of the aortic arch represent a diverse set of malformations with a common embryologic origin and a wide array of clinical manifestations. Arch anomalies are noted in 1–10/1,000 live births and account for approximately 15–20 % of all congenital heart disease (Hoffman and Kaplan, J Am Coll Cardiol 39:1890–1900, 2002). Presentation of aortic arch anomalies is highly variable with many patients remaining asymptomatic throughout life. When present, symptoms generally result from compression of surrounding mediastinal structures or associated intracardiac defects. Successful management of symptomatic arch anomalies often relies on surgical or endovascular intervention aimed at relieving compression or improving hemodynamics. In this review, we present several common aortic anomalies in correlation with their embryologic development and clinical features.

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Authors and Affiliations

  1. Division of Cardiothoracic Surgery, Columbia University, New York, NY, USA

    Scott DeRoo MD

  2. Department of Radiology, University of Michigan Health System, 1500 East Medical Center Drive, Ann Arbor, MI, 48109, USA

    Jonathan R. Dillman MD

  3. Division of Cardiothoracic Radiology, Department of Radiology, University of Michigan Health System, Cardiovascular Center 5481, Ann Arbor, MI, 48109, USA

    Philip Cascade MD

  4. Department of Cardiac Surgery, University of Michigan Health System, 1500 East Medical Center Drive, Ann Arbor, MI, 48109, USA

    Richard G. Ohye MD

  5. Division of Cardiothoracic Radiology, Department of Radiology, University of Michigan Health System, Cardiovascular Center 5481, 1500 East Medical Center Drive, Ann Arbor, MI, 48109, USA

    Baskaran Sundaram MBBS, MRCP, FRCR

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  1. Scott DeRoo MD
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  2. Jonathan R. Dillman MD
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  4. Richard G. Ohye MD
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  5. Baskaran Sundaram MBBS, MRCP, FRCR
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Correspondence to Baskaran Sundaram MBBS, MRCP, FRCR .

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  1. Department of Radiology, USC University Hospital Keck School of Medicine, Los Angeles, California, USA

    Farhood Saremi

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DeRoo, S., Dillman, J.R., Cascade, P., Ohye, R.G., Sundaram, B. (2014). Aortic Arch Anomalies. In: Saremi, F. (eds) Cardiac CT and MR for Adult Congenital Heart Disease. Springer, New York, NY. https://doi.org/10.1007/978-1-4614-8875-0_24

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