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Constriction Band Syndromes

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The Pediatric Upper Extremity

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Abstract

Constriction band syndrome is a congenital condition with a wide spectrum of clinical presentation. The physical appearance ranges from a mild hourglass-type circumferential indentation in the skin to complete digit or limb reduction. A deep band may result in distal lymphedema, nerve compression, deformity, and acrosyndactyly.

There is such great variation that no two individuals will have the identical deformity, posing a treatment challenge for hand surgeons. Operative treatment is by necessity as varied as the clinical presentation. The specific surgical strategy must be tailored to each individual and ranges from emergent limb-sparing band release to elective aesthetic band excision. Timing of surgical intervention is important and determined by the clinical presentation. Management of constriction band syndrome is focused on optimizing function, facilitating growth and development, and improving aesthetic appearance.

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Authors and Affiliations

  1. Shriners Hospital for Children, 6977 Main St, 77030, Houston, TX, USA

    Gloria Gogola

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  1. Gloria Gogola
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Correspondence to Gloria Gogola .

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Editors and Affiliations

  1. Dept. of Orthopedics, U. of Maryland School of Medicine, Timonium, Maryland, USA

    Joshua M. Abzug

  2. Shriners Hospital for Children - Phila., Philadelphia, Pennsylvania, USA

    Scott Kozin

  3. Shriners Hospital For Children - Phila., Philadelphia, Pennsylvania, USA

    Dan A. Zlotolow

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Gogola, G. (2014). Constriction Band Syndromes. In: Abzug, J., Kozin, S., Zlotolow, D. (eds) The Pediatric Upper Extremity. Springer, New York, NY. https://doi.org/10.1007/978-1-4614-8758-6_18-1

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  • DOI: https://doi.org/10.1007/978-1-4614-8758-6_18-1

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  • Online ISBN: 978-1-4614-8758-6

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