Skip to main content

Ebstein Anomaly

  • Chapter
  • First Online:
Case-Based Clinical Cardiology
  • 1116 Accesses

Abstract

Ebstein’s anomaly is an infrequent but fascinating congenital heart disorder accounting for <1% of all congenital heart disease. Since its depiction in 1866, dramatic developments in diagnosis and treatment have been made.

Ebstein’s anomaly is a complex congenital disorder with a broad pathologic-anatomical and also clinical spectrum and no two patients are identical. So, precise knowledge of the different anatomic and hemodynamic variables, related malformations and management choices are essential. Managing Ebstein’s anomaly patients is so complex. Thus, it is important that these patients are frequently seen by a cardiologist with expertise in congenital heart disease.

Here in we present a 24-year-old woman referred to our center due to frequent episodes of sudden-onset palpitation. He had a history of unknown congenital heart disease.

This is a preview of subscription content, log in via an institution to check access.

Access this chapter

eBook
USD 16.99
Price excludes VAT (USA)
  • Available as EPUB and PDF
  • Read on any device
  • Instant download
  • Own it forever
Softcover Book
USD 119.99
Price excludes VAT (USA)
  • Compact, lightweight edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info
Hardcover Book
USD 169.99
Price excludes VAT (USA)
  • Durable hardcover edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info

Tax calculation will be finalised at checkout

Purchases are for personal use only

Institutional subscriptions

References

  1. Paranon S, Acar P. Ebstein’s anomaly of the tricuspid valve: from fetus to adult: congenital heart disease. Heart. 2008;94:237–43.

    Article  Google Scholar 

  2. Ibrahim M, Tsang VT, Caruana M, et al. Cone reconstruction for Ebstein’s anomaly: patient outcomes, biventricular function, and cardiopulmonary exercise capacity. J Thorac Cardiovasc Surg. 2015;149:1144–50.

    Article  Google Scholar 

  3. Attenhofer Jost CH, Connolly HM, Dearani JA, Edwards WD, Danielson GK. Ebstein’s anomaly. Circulation. 2007;115:277–85.

    Article  Google Scholar 

  4. Yuan SM. Ebstein’s anomaly: genetics, clinical manifestations, and management. Pediatr Neonatol. 2017;58:211–5.

    Article  Google Scholar 

  5. Kron IL, Roeser ME. Management of Ebstein’s anomaly. Ann Cardiothorac Surg. 2017;6:266–9.

    Article  Google Scholar 

  6. Sadeghpour A, Alizadehasl A. The right ventricle: A comprehensive review from anatomy, physiology, and mechanics to hemodynamic, functional, and imaging evaluation. Review article. 2015;3(4):4–4. https://doi.org/10.5812/acvi.35717.

Download references

Author information

Authors and Affiliations

Authors

Editor information

Editors and Affiliations

Rights and permissions

Reprints and permissions

Copyright information

© 2021 Springer-Verlag London Ltd., part of Springer Nature

About this chapter

Check for updates. Verify currency and authenticity via CrossMark

Cite this chapter

Alizadehasl, A. (2021). Ebstein Anomaly. In: Maleki, M., Alizadehasl, A. (eds) Case-Based Clinical Cardiology. Springer, London. https://doi.org/10.1007/978-1-4471-7496-7_4

Download citation

  • DOI: https://doi.org/10.1007/978-1-4471-7496-7_4

  • Published:

  • Publisher Name: Springer, London

  • Print ISBN: 978-1-4471-7495-0

  • Online ISBN: 978-1-4471-7496-7

  • eBook Packages: MedicineMedicine (R0)

Publish with us

Policies and ethics