Abstract
Similar to many other lesions related with congenital heart disease (CHD), the terminology that surrounds double-chambered right ventricle (DCRV) has evolved over the past several decades. DCRV was initially defined more than 130 years ago. A DCRV is formed by RV obstruction due to anomalous muscle bundles. Those muscle bundles run between an area located in the ventricular septum, beneath the level of the septal leaflet of the tricuspid valve, and the anterior wall of the RV. While this can happen in isolation, it is more often part of a combination of lesions that contains DCRV, a perimembranous outlet-type ventricular septal defect, pulmonary valve stenosis, and discrete subaortic stenosis with or without aortic valve prolapse [1, 2].
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References
Restivo A, Cameron AH, Anderson RH, et al. Divided right ventricle: a review of its anatomical varieties. Pediatr Cardiol. 1984;5(3):197–204.
Byrum CJ, Dick 2nd M, Behrendt DM, et al. Excitation of the double chamber right ventricle: electrophysiologic and anatomic correlation. Am J Cardiol. 1982;49(5):1254–8.
Hubail ZJ, Ramaciotti C. Spatial relationship between the ventricular septal defect and the anomalous muscle bundle in a double-chambered right ventricle. Congenit Heart Dis. 2007;2(6):421–3.
Nagashima M, Tomino T, Satoh H, et al. Double-chambered right ventricle in adulthood. Asian Cardiovasc Thorac Ann. 2005;13(2):127–30.
Puvaneswary M, Indira N, Sreedhar M, et al. Double-chambered right ventricle: magnetic resonance imaging findings. Australas Radiol. 2005;49(2):170–4 [Medline].
Vogel M, Freedom RM, Brand A, et al. Ventricular septal defect and subaortic stenosis: an analysis of 41 patients. Am J Cardiol. 1983;52(10):1258–63.
Animasahun BA, Ekure EN, Njokanma OF. Double-chambered right ventricle: an uncommon congenital heart disease. Case report and literature review. Cardiovasc J Afr. 2011;22(5):274–7.
Romano MM, Furtado RG, Dias CG, et al. Double-chambered right ventricle in an adult patient diagnosed by transthoracic echocardiography. Cardiovasc Ultrasound. 2007;5:2.
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Video 45.1
Transthoracic echocardiography in 4 chamber shows an anomalous hypertrophied muscle bundle in mid portion of right ventricle (AVI 3012 kb)
Video 45.2
Transthoracic echocardiography short axis view showing anomalous hypertrophied muscle bundle in mid portion of right ventricle suggestive of double-chamber RV (MPG 810 kb)
Video 45.3
Transthoracic echocardiography short axis view showing anomalous hypertrophied muscle bundle in mid portion of right ventricle suggestive of double-chamber RV (MPG 1020 kb)
Transesophageal echocardiography reveals anomalous hypertrophied muscle bundle in mid portion of right ventricle suggestive of double-chamber RV with turbulent flow (MPG 1450 kb)
Transesophageal echocardiography reveals anomalous hypertrophied muscle bundle in mid portion of right ventricle suggestive of double-chamber RV with turbulent flow (MPG 1272 kb)
Typicall perimembranous VSD which is found in more than 75 % of patients with DCRV (AVI 2293 kb)
Injection at lateral view in RV shows RV muscle band at mid portion. Also contrast passage from LV to RV in recirculation is seen via VSD (WMV 1038 kb)
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Sadeghpour, A., Alizadehasl, A. (2014). Subpulmonary Right Ventricular Outflow Tract Obstruction and Double-Chambered Right Ventricle. In: Sadeghpour, A., Kyavar, M., Alizadehasl, A. (eds) Comprehensive Approach to Adult Congenital Heart Disease. Springer, London. https://doi.org/10.1007/978-1-4471-6383-1_45
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DOI: https://doi.org/10.1007/978-1-4471-6383-1_45
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