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Sudden Arrhythmic Death Syndrome and Ventricular Tachycardia in Children

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Pediatric and Congenital Cardiology, Cardiac Surgery and Intensive Care

Abstract

Sudden arrhythmogenic death in apparently healthy children is an unexpected event. Usually characterized by ventricular tachycardia devolving into ventricular fibrillation. Risk factors include congenital heart disease, cardiac channelopathies, or cardiomyopathies. The underlying mechanisms for such events are complex and poorly understood. This chapter will provide an overview of sudden arrhythmogenic death and ventricular tachycardia in children.

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Authors and Affiliations

  1. Arrhythmia, Inherited Cardiac Diseases and Sudden Death Unit, Hospital Sant Joan de Déu, Barcelona, Spain

    Georgia Sarquella-Brugada & Josep Brugada

  2. Institut de Recerca Sant Joan de Déu, Esplugues, Barcelona, Spain

    Georgia Sarquella-Brugada

  3. Medical Science Department, School of Medicine, University of Girona, Girona, Spain

    Georgia Sarquella-Brugada & Oscar Campuzano

  4. Pediatrics Department, School of Medicine, University of Barcelona, Barcelona, Spain

    Georgia Sarquella-Brugada

  5. Centro de Investigación Biomédica en Red de Enfermedades Cardiovasculares (CIBERCV), Madrid, Spain

    Oscar Campuzano & Josep Brugada

  6. Cardiovascular Genetics Center, University of Girona-IDIBGI, Girona, Spain

    Oscar Campuzano

  7. Arrhythmias Unit, Hospital Clinic, University of Barcelona, Barcelona, Spain

    Josep Brugada

  8. Cardiology Department, School of Medicine, University of Barcelona, Barcelona, Spain

    Josep Brugada

Authors
  1. Georgia Sarquella-Brugada
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  2. Oscar Campuzano
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  3. Josep Brugada
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Corresponding author

Correspondence to Georgia Sarquella-Brugada .

Editor information

Editors and Affiliations

  1. Children’s Hospital Colorado University of Colorado Denver, School of, Aurora, CO, USA

    Eduardo M. da Cruz

  2. Children's Hospital Colorado University of Colorado School of Medicin, Aurora, CO, USA

    Dunbar Ivy

  3. Department of Cardiac Surgery, German Pediatric Heart Center, Sankt Augustin, Germany

    Viktor Hraska

  4. Pediatric Cardiac Surgery, Children's Hospital Colorado University of Colorado, Aurora, CO, USA

    James Jaggers

Section Editor information

  1. No affiliation provided

    Kathryn K. Collins

  2. No affiliation provided

    Dustin Nash

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Sarquella-Brugada, G., Campuzano, O., Brugada, J. (2024). Sudden Arrhythmic Death Syndrome and Ventricular Tachycardia in Children. In: da Cruz, E.M., Ivy, D., Hraska, V., Jaggers, J. (eds) Pediatric and Congenital Cardiology, Cardiac Surgery and Intensive Care. Springer, London. https://doi.org/10.1007/978-1-4471-4999-6_138-2

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