Abstract
Pulmonary stenosis refers to either fixed or dynamic obstruction to blood flow from the pulmonary ventricle to the pulmonary arterial vasculature. The most common form of this is pulmonary valvar stenosis, which often presents in infancy but may present throughout life. Subvalvar stenosis may be in two forms, either infundibular stenosis or double-chambered right ventricle. Supravalvar stenosis may be isolated but often occurs in association with other defects like tetralogy of Fallot. Supravalvar stenosis may be associated with genetic syndromes like Williams syndrome. In the broad sense, pulmonary stenosis is present either in isolation or associated with 20–30 % of all congenital heart defects. Pulmonary valvar stenosis is most often treated with catheter-based therapy with good results. Supravalvar and subvalvar defects most commonly require surgical therapy; other lesions are more often treated surgically. In this chapter, management of these defects in the intensive care unit has some common principles that will be discussed along with the morphology and current therapy and outcomes.
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Jaggers, J., Barrett, C., Landeck, B. (2014). Pulmonary Stenosis and Insufficiency. In: Da Cruz, E., Ivy, D., Jaggers, J. (eds) Pediatric and Congenital Cardiology, Cardiac Surgery and Intensive Care. Springer, London. https://doi.org/10.1007/978-1-4471-4619-3_21
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DOI: https://doi.org/10.1007/978-1-4471-4619-3_21
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