Double Outlet Right Ventricle
- Mary Redmond HutsonAffiliated withDepartment of Pediatrics, NPRI, Duke University
- , Margaret L. KirbyAffiliated withDepartment of Pediatrics, NPRI, Duke University
DORV; Dextroposed aorta; Overriding aorta; Taussig-Bing anomaly; Tetralogy of Fallot
Definition and Characteristics
DORV encompasses a range of heart defects, in which the great vessels are misaligned with respect to the ventricles. Normally the pulmonary trunk arises from the right ventricle (RV) and aorta from the left ventricle (LV). In DORV, both the pulmonary artery and the aorta arise completely or mostly from the RV. If the aorta obtains 50% of its blood from the RV, the defect is classified as DORV . Because both outflow vessels originate predominately from the RV, there is a concomitant ventricular septal defect (VSD).
The DORV is categorized based on the position of the VSD in relation to the outflow vessels  (Fig. 1). A VSD below the aorta is called DORV with sub-aortic VSD. The great arteries are in a “side-by-side” position with the aortic valve shifted to the right of the pulmonary valve. A VSD below the pulmonary artery is ...
Reference Work Entry Metrics
- Double Outlet Right Ventricle
- Reference Work Title
- Encyclopedia of Molecular Mechanisms of Disease
- pp 543-545
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- Online ISBN
- Springer Berlin Heidelberg
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- Springer-Verlag GmbH Berlin Heidelberg
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