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IgG4-Related Disease (IgG4-RD) Presenting as a Mass in the Carotid Triangle Masquerading Paraganglioma

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Abstract

IgG4-related disease (IgG4-RD) which is a protein disorder presented as a mass in the right carotid triangle in a 30 year male patient, who underwent battery of tests is described. The radiologist opined the mass as paraganglioma and the spindle shaped character of the mass also suggested neurogenic tumor in differential diagnosis. Reference to vascular surgeon also opined the same, and adviced for incisional biopsy. Histopathology report suggested IgG4-RD and immunochemistry confirmed the final diagnosis. The neck mass which we opined as a single organ disease, proved to be multiorgan disease in PET scan.

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Acknowledgments

We thank Apollo Hospital for allowing us to use hospital records and material for preparing this manuscript.

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Authors and Affiliations

  1. Otorhinolaryngology and Head and Neck Surgery, Apollo Hospitals, Chennai, Tamil Nadu, India

    T. Ramadass, K. S. Vali Ahmed & Raees Abdurahiman

  2. 29, Pycrofts Garden Road, 2nd Floor, Flat No. 2, Ambrosia Apartments, Nungambakkam, Chennai, Tamil Nadu, 600006, India

    T. Ramadass

  3. Vascular Surgery, Apollo Hospitals, Chennai, Tamil Nadu, India

    V. Balaji

  4. Pathology, Apollo Hospitals, Chennai, Tamil Nadu, India

    S. K. J. Sheba

Authors
  1. T. Ramadass
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  2. V. Balaji
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  3. S. K. J. Sheba
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  4. K. S. Vali Ahmed
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  5. Raees Abdurahiman
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Correspondence to T. Ramadass.

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Prof. Dr. T. Ramadass, Dr. V Balaji, Dr. Sheba, Dr. Vali Ahmed, Dr. Raees declare that they have no conflict of interest.

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This article does not contain any studies with animals performed by any of the authors.

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Informed consent was obtained from the patient included in the study.

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Ramadass, T., Balaji, V., Sheba, S.K.J. et al. IgG4-Related Disease (IgG4-RD) Presenting as a Mass in the Carotid Triangle Masquerading Paraganglioma. Indian J Otolaryngol Head Neck Surg 69, 259–262 (2017). https://doi.org/10.1007/s12070-016-0976-2

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  • DOI: https://doi.org/10.1007/s12070-016-0976-2

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