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Primary Extrauterine Endometrial Stromal Cell Sarcoma: A Case and Review

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Abstract

Background

Extrauterine endometrial stromal sarcoma (ESS) is a rare neoplasm. Little is known about its pathophysiology or best treatment approach.

Case

We are describing a case of extrauterine ESS in a 70-year-old woman on hormone replacement therapy and with a history of endometriosis. We also present a brief review of the literature on ESS and its relationship to endometriosis and hormonal therapy.

Conclusions

Complete resection should remain the treatment of choice for ESS. Unresectable or metastatic low-grade ESS may respond well to progestin therapy, but outcomes of high-grade ESS tend to be poor.

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Conflict of interest statement

The authors declare that they have no conflicts of interest.

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Authors and Affiliations

  1. Stony Brook University Medical Center, Stony Brook, NY, USA

    Alla Zemlyak, Sonya Hwang, Eva Chalas & Colette R. J. Pameijer

Authors
  1. Alla Zemlyak
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  2. Sonya Hwang
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  3. Eva Chalas
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  4. Colette R. J. Pameijer
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Corresponding author

Correspondence to Colette R. J. Pameijer.

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Zemlyak, A., Hwang, S., Chalas, E. et al. Primary Extrauterine Endometrial Stromal Cell Sarcoma: A Case and Review. J Gastrointest Canc 39, 104–106 (2008). https://doi.org/10.1007/s12029-009-9064-0

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  • DOI: https://doi.org/10.1007/s12029-009-9064-0

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