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Atypical thymic carcinoid in multiple endocrine neoplasia type 1 syndrome

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Abstract

An asymptomatic, non-smoker patient carrier of a multiple endocrine neoplasya syndrome type 1 (MEN1) mutation was diagnosed with invasive atypical thymic carcinoid tumor. After surgical treatment the tumor reappeared albeit without metastasis. Thymic carcinoid is a well-known cause of mortality in MEN1, and usually metastasic disease is present at diagnosis. Male sex, smoking, and previous hyperparathyroidism probably play a role in the pathogenesis of this neoplasia.

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Authors and Affiliations

  1. Department of Endocrinology, Servicio de Endocrinología, Hospital Juan Canalejo, As Xubias 84, 15006, A Coruna, Spain

    A. Vidal, M. L. Isidro & F. Cordido

  2. Department of Pathology, Hospital Juan Canalejo, A Coruna, Spain

    M. J. Lorenzo

  3. Medicine Department, University of A Coruña, A Coruna, Spain

    F. Cordido

Authors
  1. A. Vidal
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  2. M. J. Lorenzo
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  3. M. L. Isidro
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  4. F. Cordido
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Correspondence to A. Vidal.

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Vidal, A., Lorenzo, M.J., Isidro, M.L. et al. Atypical thymic carcinoid in multiple endocrine neoplasia type 1 syndrome. J Endocrinol Invest 30, 601–602 (2007). https://doi.org/10.1007/BF03346355

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  • DOI: https://doi.org/10.1007/BF03346355

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