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Renal agenesis, ureteral ectopia into seminal vesicle, vas deferens agenesis and hemivertebra: An incomplete form of caudal regression syndrome?

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Abstract

The association of seminal vesicle cyst and upper urinary tract malformation is well known in the literature [1]. More rarely, urogenital malformations are associated with vertebral [2] or anorectal anomalies [3].

A 35-year-old infertile man with unilateral renal and deferential agenesis, seminal vesicle cyst and hemivertebra is reported.

This complex malformative syndrome has been reported previously by Sheih et al. [4] and, to our knowledge, this is the third case described in the literature.

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References

  1. Zaontz, M., Kass, E.: Ectopic ureter opening into seminal vesicle cyst associated with ipsilateral agenesis.Urology, 29, 523 (1987).

    Article  PubMed  CAS  Google Scholar 

  2. Emanuel, B., Nachman, R., Aronson, N.: Congenital solitary kidney: A review of 74 cases.Amer. J. Dis. Child., 127, 17 (1974).

    PubMed  CAS  Google Scholar 

  3. Hicks, C., Skoog, S., Done, S.: Ectopic vas deferens, imperforate anus and hypospadias: A new triad.J. Urol., 141, 586 (1989).

    PubMed  CAS  Google Scholar 

  4. Sheih, C., Liao, Y., Li, Y., Yang, L.: Seminal vesicle cyst associated with ipsilateral renal malformation and hemivertebra: Report of 2 cases.J. Urol., 150, 1214 (1993).

    PubMed  CAS  Google Scholar 

  5. Stephens, F. D.: Congenital Malformations of the Urinary Tract. Praeger, New York 1983, pp. 185–206.

    Google Scholar 

  6. Mackie, G., Stephens, F.: Duplex kidneys: A correlation of renal dysplasia with position of the ureteral orifice.J. Urol., 114, 274 (1975).

    PubMed  CAS  Google Scholar 

  7. Schwarz, R., Stephens, F.: The persisting mesonephric duct: High junction of vas deferens and ureter.J. Urol., 120, 592 (1978).

    PubMed  CAS  Google Scholar 

  8. Duhamel, B.: From the mermaid to anal imperforation: The syndrome of caudal regressionArch. Dis. Child., 36, 152, (1961).

    Google Scholar 

  9. King, B., Hattery, R., Lieber, M., Berquist, T., Williamson, B., Hartman, G.: Congenital cystic disease of the seminal vesicle.Radiology, 178, 207 (1991).

    PubMed  CAS  Google Scholar 

  10. Sheih, C., Hung, C., Wei, C., Lin, C.: Cystic dilatations within the pelvis in patients with ipsilateral renal agenesis or dysplasia.J. Urol., 144, 324 (1990).

    PubMed  CAS  Google Scholar 

  11. Deane, A., May, R.: Absent vas deferens in association with renal abnormalities.Br. J. Urol., 54, 298 (1982).

    PubMed  CAS  Google Scholar 

  12. Lukash, F., Zwiren, G., Andrews, H.: Significance of absent vas deferens at hernia repair in infants and children.J. Pediatr. Surg., 10, 765 (1975).

    Article  PubMed  CAS  Google Scholar 

  13. Weyman, P. J., Mc Clennan, B. L.: Computed tomography and ultrasonography in the evaluation of mesonephric duct anomalies.Urol. Radiol., 1, 29 (1984).

    Article  Google Scholar 

  14. Kneeland, J. B., Auh, Y. H., McCarron, J. P., Zirinski, K., Rubistein, W. A., Kazam, E.: Computed tomography, sonography, vesiculography and M.R. imaging of a seminal vesicle cyst.J.C.A.T., 9, 964 (1985).

    CAS  Google Scholar 

  15. Genevois, P. A., Van Regemorter, G., Van Gansbeke, D., Kuhn, G., Struyven, J.: Kyste de la vésicule séminale. Aspects en échotomographie, tomodensitométrie et résonance magnetique nucleaire. A propos d'un cas.J. Radiol., 68, 489 (1987).

    Google Scholar 

  16. Mayersak, J. S.: Urogenital sinus-ejaculatory duct cyst: A case report with a proposed clinical classification and review of the literature.J. Urol., 142, 1330 (1989).

    PubMed  CAS  Google Scholar 

  17. Desgrez, J. P.: Malformation kystiques infectées d'une vésicule avec agénésie uréterorénale ipsilatérale. Description, discussion de la voie d'abord chirurgicale.Ann. Urol., 20, 411 (1986).

    CAS  Google Scholar 

  18. Roehrborn, C. G., Schneider, H. J., Rugendorff, E. W., Hamann, W.: Embryological and diagnostic aspects of seminal vesicle cysts associated with upper urinary tract malformation.J. Urol., 135, 1029 (1986).

    PubMed  CAS  Google Scholar 

  19. Meacham, R. B., Hellerstein, D. K., Lipshultz, L. I.: Evaluation and treatment of ejaculatory duct obstruction in the infertile male.Fertil. Steril., 59, 393 (1993).

    PubMed  CAS  Google Scholar 

  20. Goluboff, E. T., Stifelman, M. D., Fish, H.: Ejaculatory duct obstruction in the infertile male.Urology, 45 (6), 925 (1995).

    Article  PubMed  CAS  Google Scholar 

  21. Legeais, D., Duquens, G.: Un kyste gèant de la vésicule séminale associé à une agénésie urétero-rénale ipsilatérale.Progr. Urol., 4, 256 (1994).

    CAS  Google Scholar 

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Authors and Affiliations

  1. Institute of Urology, University of Padua, Italy

    F. Aragona, L. D'Urso, C. Valotto, C. Milani & A. Calabro

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  1. F. Aragona
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  2. L. D'Urso
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  3. C. Valotto
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  4. C. Milani
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  5. A. Calabro
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Aragona, F., D'Urso, L., Valotto, C. et al. Renal agenesis, ureteral ectopia into seminal vesicle, vas deferens agenesis and hemivertebra: An incomplete form of caudal regression syndrome?. International Urology and Nephrology 29, 403–410 (1997). https://doi.org/10.1007/BF02551104

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