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Budd-Chiari Syndrome pp 171–179Cite as

Surgery for Budd–Chiari Syndrome

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Abstract

Budd–Chiari syndrome (BCS) is the disease which represented by an obstruction in the hepatic venous outflow from small hepatic veins to the inferior vena cava (IVC) caused by thrombosis or fibrous sequelae. BCS is a rare disease with an incidence of 0.1 to 10 per million inhabitants a year whose etiological factors include hypercoagulable conditions, myeloprolipherative diseases, anatomical variability of IVC, and environmental conditions. The treatment for BCS contains multi-step management. Initially anticoagulation therapy has tended to be chosen. In patients without any recovery of symptom after anticoagulation therapy, interventional revascularization and the transjugular intrahepatic portosystemic shunt procedure are indicated, whereas IVC plasty with a patch graft and cavo-right atrium, portosystemic shunt is indicated for obstruction of the IVC. The patency of IVC plasty and bypass has been reported as satisfactory. Long-term outcomes after surgical procedures are sustainable but the risk of hepatocellular carcinoma occurrence has been a problem in long-term follow-up. Liver transplantation is usually indicated as a treatment in patients who develop liver failure despite undergoing various treatments.

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Abbreviations

BCS:

Budd–Chiari syndrome

IVR:

Interventional radiology

PTA:

Percutaneous transluminal angioplasty

TIPS:

Transjugular intrahepatic portosystemic shunt

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Authors and Affiliations

  1. Department of Surgery, Nagasaki University Graduate School of Biomedical Sciences, Nagasaki, Japan

    Masaaki Hidaka & Susumu Eguchi

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  1. Masaaki Hidaka
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  2. Susumu Eguchi
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Corresponding author

Correspondence to Susumu Eguchi .

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Editors and Affiliations

  1. Department of Gastroenterology, General Hospital of Northern Theater Command, Shenyang, Liaoning, China

    Xingshun Qi

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Hidaka, M., Eguchi, S. (2020). Surgery for Budd–Chiari Syndrome. In: Qi, X. (eds) Budd-Chiari Syndrome. Springer, Singapore. https://doi.org/10.1007/978-981-32-9232-1_13

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  • DOI: https://doi.org/10.1007/978-981-32-9232-1_13

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  • Publisher Name: Springer, Singapore

  • Print ISBN: 978-981-32-9231-4

  • Online ISBN: 978-981-32-9232-1

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