Abstract
Acquired cystic kidney disease (ACKD) is a well-described condition in the adult population, which occurs primarily in patients with end-stage renal disease (ESRD). In contrast to inherited cystic kidney disease, ACKD is characterized by the presence of multiple small cysts in small kidneys. Whereas pediatric data pertaining to the development of ACKD is limited, a high incidence (21.6–45.8%) of the disorder has been described in children on chronic dialysis. An increased frequency of ACKD is also associated with a longer duration of dialysis. Although most patients with ACKD are asymptomatic, the condition can be complicated by the development of renal cell carcinoma (RCC). Since early RCC detection can lead to improved long-term outcome, routine surveillance should be considered in pediatric dialysis and transplant recipients.
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Chan, E.Y.H., Warady, B.A. (2017). Acquired Cystic Kidney Disease. In: Warady, B., Schaefer, F., Alexander, S. (eds) Pediatric Dialysis Case Studies. Springer, Cham. https://doi.org/10.1007/978-3-319-55147-0_44
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DOI: https://doi.org/10.1007/978-3-319-55147-0_44
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