Abstract
Surgical treatment of children with OI in India often needs to be tailored to the needs of patients who have limited finances and access to care. The surgeon needs to find ways of reducing costs and also deal with the consequences of delay in treatment due to financial constraints. Costs can be reduced considerably by using inexpensive implants and simple techniques; an example is dual Rush rodding of the femur. Delayed treatment may result in severe deformities and the surgeon needs to be conversant with techniques to deal with them. The surgeon needs to be aware of complications that can develop due to delay in treatment of fractures and treat such fractures early in order to prevent serious complications that are difficult to treat; an example is intramedullary rodding of a humeral fracture to prevent a gap non-union of the humerus. Finally, the surgeon dealing with OI should be aware of the extremely debilitating consequences and the very poor quality of life of patients with severe OI who have had no access to treatment.
Access this chapter
Tax calculation will be finalised at checkout
Purchases are for personal use only
References
Joseph B, Rebello G, Kant BC. The choice of intramedullary devices for the femur and the tibia in osteogenesis imperfecta. J Pediatr Orthop B. 2005;14:311–9.
Stephen J, Shukla A, Dalal A, Girisha KM, Shah H, Gupta N, Kabra M, Dabadghao P, Phadke SR. 2014. Mutation spectrum of COL1A1 and COL1A2 genes in Indian patients with osteogenesisimperfecta. Am J Med Genet Part A. 2014;164A:1482–9.
Stephen J, Girisha KM, Dalal A, Shukla A, Shah H, Srivastava P, Kornak U, Phadke SR. Mutations in patients with osteogenesis imperfecta from consanguineous Indian families. Eur J Med Genet. 2015;58:21–7.
Mrosk J, Bhavani GS, Shah H, Hecht J, Krüger U, Shukla A, Kornak U, Girisha KM. Diagnostic strategies and genotype-phenotype correlation in a large Indian cohort of osteogenesis imperfecta. Bone. 2018;110:368–77.
Mulpuri K, Joseph B. Intramedullary rodding in osteogenesis imperfecta. J Pediatr Orthop. 2000;20(2):267–73.
Joseph B, Shah H, Siddesh ND. A simple, safe and inexpensive way to apply hip spica casts in children. Tips and Techniques. www.global-help.org
Agarwal V, Joseph B. Non-union in osteogenesis imperfecta. J Pediatr Orthop B. 2005;14(6):451–5.
Franzone JM, Bober MB, Rogers KJ, McGreal CM, Kruse RW. Re-alignment and intramedullary rodding of the humerus and forearm in children with osteogenesis imperfecta: revision rate and effect on fracture rate. J Child Orthop. 2017;11:185–90.
Lin D, Zhai W, Lian K, Ding Z. Results of a bone splint technique for the treatment of lower limb deformities in children with type I osteogenesis imperfecta. Indian J Orthop. 2013;47:377–81.
Wenger DR, Abrams RA, Yaru N, Leach J. Obstruction of the colon due to protrusion acetabuli in osteogenesis imperfecta: treatment by pelvic osteotomy. Report of a case. J Bone Joint Surg Am. 1988;70:1103–7.
Author information
Authors and Affiliations
Editor information
Editors and Affiliations
Rights and permissions
Copyright information
© 2020 Springer Nature Switzerland AG
About this chapter
Cite this chapter
Shah, H., Joseph, B. (2020). Management of Osteogenesis Imperfecta in India. In: Kruse, R. (eds) Osteogenesis Imperfecta. Springer, Cham. https://doi.org/10.1007/978-3-030-42527-2_16
Download citation
DOI: https://doi.org/10.1007/978-3-030-42527-2_16
Published:
Publisher Name: Springer, Cham
Print ISBN: 978-3-030-42526-5
Online ISBN: 978-3-030-42527-2
eBook Packages: MedicineMedicine (R0)