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Clinical Ophthalmic Oncology pp 239–248Cite as

Orbital Retinoblastoma: Diagnosis and Management

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Abstract

Orbital retinoblastoma is a potentially fatal disease. It is more prevalent in the developing world where delay in presentation and lack of access to healthcare contribute to poor survival rates. However, with the evolution of a multimodal therapy, the prognosis for survival has improved significantly. The current treatment protocols use a combination of high-dose systemic chemotherapy, followed by appropriate surgery, radiotherapy, and adjuvant chemotherapy. This chapter discusses in detail the clinical spectrum of orbital retinoblastoma, classification and subtypes, evaluation and investigations, strategies for management, and future perspectives.

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Author information

Authors and Affiliations

  1. Ocular Oncology Service Dr. Rajendra Prasad Centre for Ophthalmic Sciences, New Delhi, India

    Bhavna Chawla

  2. Department of Ophthalmology, SMS Medical College & Hospital, Jaipur, Rajasthan, India

    Maya Hada

Authors
  1. Bhavna Chawla
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  2. Maya Hada
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Editor information

Editors and Affiliations

  1. Associate Professor of Ophthalmology, Children’s Hospital Los Angeles, The USC Roski Eye Institute Keck School of Medicine, Los Angeles, CA, USA

    Jesse L. Berry

  2. Children’s Hospital Los Angeles, The USC Roski Eye Institute, Keck School of Medicine, Los Angeles, CA, USA

    Jonathan W. Kim

  3. University of Oxford, Nuffield Department of Clinical Neurosciences, John Radcliffe Hospital, Oxford, UK

    Bertil E. Damato

  4. Department of Ophthalmic Oncology, Cole Eye Institute, Cleveland Clinic, Cleveland, OH, USA

    Arun D. Singh

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Chawla, B., Hada, M. (2019). Orbital Retinoblastoma: Diagnosis and Management. In: Berry, J., Kim, J., Damato, B., Singh, A. (eds) Clinical Ophthalmic Oncology. Springer, Cham. https://doi.org/10.1007/978-3-030-11123-6_20

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  • DOI: https://doi.org/10.1007/978-3-030-11123-6_20

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-11122-9

  • Online ISBN: 978-3-030-11123-6

  • eBook Packages: MedicineMedicine (R0)

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