Abstract
Extraskeletal myxoid chondrosarcoma (EMC) is a relatively slow-growing soft tissue sarcoma that often presents with metastatic disease, typically innumerable round lung nodules of varying sizes that also grow slowly but relentlessly [1, 2]. It is different in all genetic and histopathological aspects from skeletal chondrosarcoma [3]. EMC typically affects people between ages 30 and 60 [1, 4] (Fig. 20.1) and occurs most commonly in the lower extremity (Fig. 20.2). Men are affected more commonly than women, but there does not appear to be a difference in incidence based on race [5]. Tumors present as painless, slow-growing multi-lobulated masses and are soft, gelatinous in consistency, and often hemorrhagic.
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Brennan, M.F., Antonescu, C.R., Maki, R.G. (2013). Extraskeletal Myxoid Chondrosarcoma. In: Management of Soft Tissue Sarcoma. Springer, New York, NY. https://doi.org/10.1007/978-1-4614-5004-7_20
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DOI: https://doi.org/10.1007/978-1-4614-5004-7_20
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