Retinal degenerations are a leading cause of blindness in many parts of the world (Bunker et al., 1984; Grondahl, 1987; Berson, 1993; Klein et al., 1995; Attebo et al., 1996; Klaver et al., 1998; Novak-Laus et al., 2002). In the United States an estimated 6 million people have age-related macular degeneration with a decrease in central vision after age 60. About 100,000 people have retinitis pigmentosa or a related disease with loss of side and night vision in adolescence; they often develop tunnel vision by age 40 and lose central vision by age 60.
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Berson, E.L. (2008). Retinal Degenerations: Planning for the Future. In: Anderson, R.E., LaVail, M.M., Hollyfield, J.G. (eds) Recent Advances in Retinal Degeneration. Advances in Experimental Medicine and Biology, vol 613. Springer, New York, NY. https://doi.org/10.1007/978-0-387-74904-4_2
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