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Adrenal Tumors

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Book cover What’s New in Surgical Oncology

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Abstract

Adrenocortical tumors (ACTs) are common, with an estimated prevalence of 7.3% in autopsy cases [1], A computed tomography (CT) study reported an overall prevalence of 4.4% of adrenal lesions in a population aged > 50 years [2]. In contrast, adrenocortical cancer (ACC) is a rare malignancy with an estimated incidence of 4–12 per million population and a variable (but generally poor) prognosis. Women are more often affected than men (ratio 1.5:1) [3]. An exceptionally high annual incidence of ACC has been reported for children in southern Brazil (3.4–4.2 per million children vs an estimated worldwide incidence of 0.3 per million children younger than 15 years) and is related to a mutation in the TP53 tumor suppressor gene. The age distribution is reported to be bimodal with a first peak in childhood and a second higher peak in the fourth and fifth decade.

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Authors and Affiliations

  1. General Surgery, Gorizia Hospital, Gorizia, Italy

    Domenico Capizzi & Alfredo Miseri

  2. General, Emergency and Minimally Invasive Surgery, Careggi Hospital, Florence, Italy

    Carlo Bergamini, Jacopo Martellucci, Tatiana Bargellini, Ancuta Leahu & Andrea Valeri

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  1. Carlo Bergamini
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  2. Jacopo Martellucci
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  7. Andrea Valeri
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Correspondence to Carlo Bergamini .

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  1. General, Emergency and Minimally Invasive Surgery, Careggi Hospital, Florence, Italy

    Andrea Valeri , Carlo Bergamini  & Jacopo Martellucci ,  & 

  2. Local Healthcare Unit ULSS 19 - Veneto, Adria, Italy

    Ferdinando Agresta

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Bergamini, C. et al. (2013). Adrenal Tumors. In: Valeri, A., Bergamini, C., Agresta, F., Martellucci, J. (eds) What’s New in Surgical Oncology. Springer, Milano. https://doi.org/10.1007/978-88-470-5310-6_10

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  • DOI: https://doi.org/10.1007/978-88-470-5310-6_10

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