Abstract
Ebstein’s anomaly is a congenital malformation of the tricuspid valve and right ventricle characterized by several features, each of which can exhibit a spectrum of malformations relevant to the surgical management of the condition:
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displacement of the septal and posterior leaflets of the tricuspid valve towards the apex of the right ventricle, with adherence to the myocardium
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anterior leaflet attached to the appropriate level of the tricuspid valve annulus, however, redundant, larger than normal and with multiple fenestrations and chordal attachments to the ventricular wall
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segment of the right ventricle from the level of true tricuspid annulus to the level of attachment of the septal and posterior leaflets unusually thin and dysplastic, and described as “atrialized”; right atrio-ventricular junction (being the true tricuspid valvular annulus) and right atrium extremely dilated
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cavity of the right ventricle, beyond the atrialized portion, reduced in size, usually with lack of an inlet chamber, and with a small trabecular component
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infundibulum often obstructed by the redundant tissue of the anterior leaflet as well as by the chordal attachments of the anterior leaflet to the infundibulum
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variable type and degree of ventricular dysfunction.
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(2009). Ebstein’s anomaly. In: Congenital Heart Defects. Steinkopff. https://doi.org/10.1007/978-3-7985-1719-6_11
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DOI: https://doi.org/10.1007/978-3-7985-1719-6_11
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