Résumé
L’homocystéine est un acide aminé non protéique qui apparaît comme intermédiaire dans le métabolisme des acides aminés soufrés. C’est le produit de déméthylation de la méthionine. Il peut soit donner de la cystéine dans la voie de la transsulfuration, soit redonner de la méthionine dans la voie de la reméthylation [1] (Figure 1).
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De Lonlay, P., Dubois, S., Valayannopoulos, V., Depondt, E., Ottolenghi, C., Rabier, D. (2013). Homocystinurie, métabolisme des folates et de la B12. In: Prise en charge médicale et diététique des maladies héréditaires du métabolisme. Springer, Paris. https://doi.org/10.1007/978-2-8178-0046-2_12
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DOI: https://doi.org/10.1007/978-2-8178-0046-2_12
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