Abstract
Restrictive cardiomyopathy is a condition characterized by normal left ventricular cavity size and systolic function but with increased myocardial stiffness [1]. This makes the ventricle incompliant and fill predominantly in early diastole. When atrial systolic function is maintained, the ventricle may accommodate a small volume of blood during atrial systole but at the expense of further raising the end diastolic pressure. These physiological disturbances are associated with raised left atrial pressure, atrial dilatation, and possible arrhythmias [2].
This is a preview of subscription content, log in via an institution to check access.
Access this chapter
Tax calculation will be finalised at checkout
Purchases are for personal use only
References
Siegel RJ, Shah PK, Fishbein MC. Idiopathic restrictive cardiomyopathy. Circulation. 1984;70(2):165–9.
Benotti JR, Grossman W, Cohn PF. Clinical profile of restrictive cardiomyopathy. Circulation. 1980;61(6):1206–12.
Roberts WC, Liegler DG, Carbone PP. Endomyocardial disease and eosinophilia. A clinical and pathologic spectrum. Am J Med. 1969;46(1):28–42.
Candell-Riera J, Permanyer-Miralda G, Soler-Soler J. EchocarÂdiographic findings in endomyocardial fibrosis. Chest. 1982;82(1):88–90.
Child JS, Levisman JA, Abbasi AS, MacAlpin RN. EchocarÂdiographic manifestations of infiltrative cardiomyopathy. A report of seven cases due to amyloid. Chest. 1976;70(6):726–31.
Cueto-Garcia L, Tajik AJ, Kyle RA, Edwards WD, Greipp PR, Callahan JA, et al. Serial echocardiographic observations in patients with primary systemic amyloidosis: an introduction to the concept of early (asymptomatic) amyloid infiltration of the heart. Mayo Clin Proc. 1984;59(9):589–97.
Silverman KJ, Hutchins GM, Bulkley BH. Cardiac sarcoid: a clinicopathologic study of 84 unselected patients with systemic sarcoidosis. Circulation. 1978;58(6):1204–11.
Short EM, Winkle RA, Billingham ME. Myocardial involvement in idiopathic hemochromatosis. Morphologic and clinical improvement following venesection. Am J Med. 1981;70(6):1275–9.
Henein MY, Gibson DG. Abnormal subendocardial function in restrictive left ventricular disease. Br Heart J. 1994;72(3):237–42.
Henein M, Lindqvist P, Mörner S, Henein MY. Effect of raised left atrial pressure on its regional and segmental chamber function: the role of speckle tracking. Scand Cardiovasc J. 2009;43:8.
Schneider MP, Hua TA, Böhm M, Wachtell K, Kjeldsen SE, Schmieder RE. Prevention of atrial fibrillation by renin-angiotensin system inhibition. J Am Coll Cardiol. 2010;55:2299–307.
Hess OM, Turina M, Senning A, Goebel NH, Scholer Y, Krayenbuehl HP. Pre- and postoperative findings in patients with endomyocardial fibrosis. Br Heart J. 1978;40(4):406–15.
George BO, Gaba FE, Talabi AI. M-mode echocardiographic features of endomyocardial fibrosis. Br Heart J. 1982;48(3):222–8.
Vijayaraghavan G, Davies J, Sadanandan S, Spry CJ, Gibson DG, Goodwin JF. Echocardiographic features of tropical endomyocardial disease in South India. Br Heart J. 1983;50(5):450–9.
Acquatella H, Schiller NB, Puigbo JJ, Gomez-Mancebo JR, Suarez C, Acquatella G. Value of two-dimensional echocardiography in endomyocardial disease with and without eosinophilia. A clinical and pathologic study. Circulation. 1983;67(6):1219–26.
Davies J, Gibson DG, Foale R, Heer K, Spry CJ, Oakley CM, et al. Echocardiographic features of eosinophilic endomyocardial disease. Br Heart J. 1982;48(5):434–40.
Gottdiener JS, Maron BJ, Schooley RT, Harley JB, Roberts WC, Fauci AS. Two-dimensional echocardiographic assessment of the idiopathic hypereosinophilic syndrome. Anatomic basis of mitral regurgitation and peripheral embolization. Circulation. 1983;67(3):572–8.
Olson LJ, Baldus WP, Tajik AJ. Echocardiographic features of idiopathic hemochromatosis. Am J Cardiol. 1987;60(10):885–9.
Hwang B, Meng CC, Lin CY, Hsu HC. Clinical analysis of five infants with glycogen storage disease of the heart–Pompe’s disease. Jpn Heart J. 1986;27(1):25–34.
Bass JL, Shrivastava S, Grabowski GA, Desnick RJ, Moller JH. The M-mode echocardiogram in Fabry’s disease. Am Heart J. 1980;100(6 Pt 1):807–12.
Cueto-Garcia L, Reeder GS, Kyle RA, Wood DL, Seward JB, Naessens J, et al. Echocardiographic findings in systemic amyloidosis: spectrum of cardiac involvement and relation to survival. J Am Coll Cardiol. 1985;6(4):737–43.
Siqueira-Filho AG, Cunha CL, Tajik AJ, Seward JB, Schattenberg TT, Giuliani ER. M-mode and two-dimensional echocardiographic features in cardiac amyloidosis. Circulation. 1981;63(1):188–96.
Klein AL, Hatle LK, Burstow DJ, Seward JB, Kyle RA, Bailey KR, et al. Doppler characterization of left ventricular diastolic function in cardiac amyloidosis. J Am Coll Cardiol. 1989;13(5):1017–26.
Henein MY, Amadi A, O’Sullivan C, Coats A, Gibson DG. ACE inhibitors unmask incoordinate diastolic wall motion in restrictive left ventricular disease. Heart. 1996;76(4):326–31.
Child JS, Krivokapich J, Abbasi AS. Increased right ventricular wall thickness on echocardiography in amyloid infiltrative cardiomyopathy. Am J Cardiol. 1979;44(7):1391–5.
Klein AL, Hatle LK, Taliercio CP, Oh JK, Kyle RA, Gertz MA, et al. Prognostic significance of Doppler measures of diastolic function in cardiac amyloidosis. A Doppler echocardiography study. Circulation. 1991;83(3):808–16.
Chandrasekaran K, Aylward PE, Fleagle SR, Burns TL, Seward JB, Tajik AJ, et al. Feasibility of identifying amyloid and hypertrophic cardiomyopathy with the use of computerized quantitative texture analysis of clinical echocardiographic data. J Am Coll Cardiol. 1989;13(4):832–40.
Saraia M, Costa P, Birken S, Goodman S. Presence of an abnormal transthyretin (prealbumin) in Portuguese patients with familial amyloidotic polyneuropathy. Trans Assoc Am Physicians. 1983;96:261–70.
Connors LH, Lim A, Prokaeva T, Roskens VA, Costello CE. Tabulation of human transthyretin (TTR) variants. Amyloid. 2003;10:160–84.
Ando Y, Suhr OB. Autonomic dysfunction in familial amyloidotic polyneuropathy (FAP). Amyloid. 1998;5:288–300.
Backman C, Olofsson BO. Echocardiographic features in familial amyloidosis with polyneuropathy. Acta Med Scand. 1983;214:273–8.
Olofsson BO, Backman C, Boman K. Familial amyloidotic polyneuropathy in northern Sweden. A cross-sectional and longitudinal study of cardiac function with echocardiography. Arctic Med Res. 1988;47 Suppl 1:423–5.
Wiklund U, Hörnsten R, Karlsson M, Suhr OB, Jensen SM. Abnormal heart rate variability and subtle atrial arrhythmia in patients with familial amyloidotic polyneuropathy. Ann Noninvasive Eletrocardiol. 2008;13:249–56.
Zhao Y, Hörnsten R, Lindqvist P, Wiklund U, Suhr OB, Henein MY. Left ventricular dyssynchrony is associated with reduced heart rate variability in familial amyloidotic polyneuropathy. Int J Cardiol. 2010 Nov-4 e-pub ahead of print
Lewin RF, Mor R, Spitzer S, Arditti A, Hellman C, Agmon J. Echocardiographic evaluation of patients with systemic sarcoidosis. Am Heart J. 1985;110(1 Pt 1):116–22.
Candell-Riera J, Lu L, Seres L, Gonzalez JB, Batlle J, Permanyer-Miralda G, et al. Cardiac hemochromatosis: beneficial effects of iron removal therapy. An echocardiographic study. Am J Cardiol. 1983;52(7):824–9.
Author information
Authors and Affiliations
Corresponding author
Editor information
Editors and Affiliations
Electronic Supplementary material
Parasternal long axis views form a patient with amyloid heart disease
video.avi (2,929 KB)
Rights and permissions
Copyright information
© 2012 Springer-Verlag London Limited
About this chapter
Cite this chapter
Henein, M.Y., Sheppard, M. (2012). Restrictive Cardiomyopathy. In: Henein, M. (eds) Clinical Echocardiography. Springer, London. https://doi.org/10.1007/978-1-84882-521-5_11
Download citation
DOI: https://doi.org/10.1007/978-1-84882-521-5_11
Published:
Publisher Name: Springer, London
Print ISBN: 978-1-84882-520-8
Online ISBN: 978-1-84882-521-5
eBook Packages: MedicineMedicine (R0)