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Endocrine Tumors and Tumor-Like Lesions of Infancy, Childhood, and Adolescents and Inherited Tumor Syndromes

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Abstract

The endocrine system is an embryological diverse system composed of a variety of glands, such as pituitary, pineal, thyroid, parathyroid, adrenal, endocrine pancreas, and the diffuse neuroendocrine system. Neoplasms of all of these organs seen in adults are also found in infancy, childhood, and adolescents, both sporadic and as part of an inherited tumor syndrome. Besides these neoplastic diseases, young children and adolescents may present with a mass-like lesion that may be developmental or an embryological defect in nature and may mimic neoplasms. These diseases may include enlargement and hyperplasia, a single mass, or atrophy accompanied by hypofunction. We will discuss some of the different types of pathology that occur in adults and may also be present in infancy, childhood, and adolescents, as well as, tumors and tumor-like conditions that occur almost exclusively in these groups. We will cover also sporadic tumors and tumors occurring in a familial setting.

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Correspondence to Vânia Nosé .

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Nosé, V. (2009). Endocrine Tumors and Tumor-Like Lesions of Infancy, Childhood, and Adolescents and Inherited Tumor Syndromes. In: Khan, A. (eds) Surgical Pathology of Endocrine and Neuroendocrine Tumors. Current Clinical Pathology. Humana Press. https://doi.org/10.1007/978-1-60327-396-1_17

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  • DOI: https://doi.org/10.1007/978-1-60327-396-1_17

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