Abstract
Rhabdomyosarcoma is a malignant mesenchymal neoplasm with skeletal muscle differentiation that typically occurs in the deep soft tissue or viscera. Three subtypes comprise the majority of cases of rhabdomyosarcoma: embryonal, alveolar, and pleomorphic. All three types may very rarely occur as primary tumors arising in the skin or subcutis without deep soft tissue involvement. Other uncommon subtypes, such as epithelioid rhabdomyosarcoma, also exist and may occur in the skin, as well. Less than 50 cases of primary cutaneous rhabdomyosarcoma (PC-RMS) have been reported.
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Gardner, J.M., Smoller, B.R. (2015). Primary Cutaneous Rhabdomyosarcoma. In: Rare Malignant Skin Tumors. Springer, New York, NY. https://doi.org/10.1007/978-1-4939-2023-5_43
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DOI: https://doi.org/10.1007/978-1-4939-2023-5_43
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