Skip to main content

Psychosexual Quality of Life in Adult Intersexuality: The Example of Congenital Adrenal Hyperplasia (CAH)

An Invited Contribution

  • Conference paper
Therapeutic Outcome of Endocrine Disorders

Abstract

A fundamental aspect of the quality of life in adolescence and adulthood is psychosexuality. It comprises three interrelated aspects: (1) gender role behavior and gender identity; (2) sexual life, with its four components of sexual orientation, courtship, partner bonding, and genital sexuality; (3) reproduction and parenting. Intersexuality tends to affect all three aspects of psychosexuality. In this chapter, we will use data on the syndrome of classical congenital adrenal hyperplasia (CAH) in 46,XX individuals with 21-hydroxylase deficiency as an illustrative example.

This is a preview of subscription content, log in via an institution to check access.

Access this chapter

Chapter
USD 29.95
Price excludes VAT (USA)
  • Available as PDF
  • Read on any device
  • Instant download
  • Own it forever
eBook
USD 79.99
Price excludes VAT (USA)
  • Available as EPUB and PDF
  • Read on any device
  • Instant download
  • Own it forever
Softcover Book
USD 99.99
Price excludes VAT (USA)
  • Compact, lightweight edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info

Tax calculation will be finalised at checkout

Purchases are for personal use only

Institutional subscriptions

Preview

Unable to display preview. Download preview PDF.

Unable to display preview. Download preview PDF.

References

  1. Money J, Ehrhardt AA. Man and woman, boy and girl: Differentiation and dimorphism of gender identity from conception to maturity. Baltimore (MD): Johns Hopkins University Press, 1972.

    Google Scholar 

  2. Berenbaum S. Psychological outcome in congenital adrenal hyperplasia. In: Stabler B, Bercu BB, editors. Therapeutic outcome of endocrine disorders: efficacy, innovation and quality of life. New York: Springer-Verlag, 2000: 186–99.

    Chapter  Google Scholar 

  3. Dittmann RW, Kappes MH, Kappes ME, Börger D, Meyer-Bahlburg HFL, Stegner H, et al. Congenital adrenal hyperplasia II: gender-related behavior and attitudes in female salt-wasting and simple-virilizing patients. Psychoneuroendocrinology 1990; 15: 421–34.

    Article  PubMed  CAS  Google Scholar 

  4. Meyer-Bahlburg HFL, Gruen RS, New MI, Bell JJ, Morishima A, Shimshi M, et al. Gender change from female to male in classical CAH. Horm Behav 1996; 30: 319–32.

    Article  PubMed  CAS  Google Scholar 

  5. Mulaikal RM, Migeon CJ, Rock JA. Fertility rates in female patients with congenital adrenal hyperplasia due to 21-hydroxylase deficiency. New Engl JMed 1987; 316: 178–82.

    Article  CAS  Google Scholar 

  6. Federman DD. Psychosexual adjustment in congenital adrenal hyperplasia [editorial]. New Engl JMed 1987; 316: 209–11.

    Article  CAS  Google Scholar 

  7. Money J, Devore H, Norman BF. Gender identity and gender transposition: longitudinal outcome study of 32 male hermaphrodites assigned as girls. J Sex Marital Ther 1986; 12: 165–81.

    Article  PubMed  CAS  Google Scholar 

  8. Meyer-Bahlburg HFL, Ehrhardt AA, Rosen LR, Gruen RS, Veridiano NP, Vann FH, et al. Prenatal estrogens and the development of homosexual orientation. Dev Psychol 1995; 31: 12–21.

    Article  Google Scholar 

  9. Lish JD, Ehrhardt AA, Meyer-Bahlburg HFL, Rosen LR, Gruen RS, Veridiano NP. Gender-related behavior development in females exposed to diethylstilbestrol (DES) in utero: an attempted replication. J Am Acad Child Adol Psychiatr 1991; 30: 29–37.

    Article  CAS  Google Scholar 

  10. Meyer-Bahlburg HFL, Ehrhardt AA. Sexual behavior assessment schedule-adult (SEBAS-A). New York: Authors 1983. Available through the Columbia University College of Physicians and Surgeons.

    Google Scholar 

  11. Kuhnle U, Bullinger M, Schwarz HP. The quality of life in adult female patients with congenital adrenal hyperplasia: a comprehensive study of the impact of genital malformations and chronic disease on female patients life. Eur J Pediatr 1995; 154: 708–16.

    Article  PubMed  CAS  Google Scholar 

Download references

Authors

Editor information

Editors and Affiliations

Rights and permissions

Reprints and permissions

Copyright information

© 2000 Springer Science+Business Media New York

About this paper

Cite this paper

Meyer-Bahlburg, H.F.L. et al. (2000). Psychosexual Quality of Life in Adult Intersexuality: The Example of Congenital Adrenal Hyperplasia (CAH). In: Stabler, B., Bercu, B.B. (eds) Therapeutic Outcome of Endocrine Disorders. Serono Symposia USA. Springer, New York, NY. https://doi.org/10.1007/978-1-4612-1230-0_20

Download citation

  • DOI: https://doi.org/10.1007/978-1-4612-1230-0_20

  • Publisher Name: Springer, New York, NY

  • Print ISBN: 978-1-4612-7052-2

  • Online ISBN: 978-1-4612-1230-0

  • eBook Packages: Springer Book Archive

Publish with us

Policies and ethics