Abstract
Embryonal tumors at extracerebellar sites are composed of undifferentiated neuroepithelial cells with capacity for divergent differentiation, including neuronal, astrocytic, myoid, or melanocytic differentiation. Tumors may recapitulate the primitive neural tube (medulloepithelioma) or have ependymoblastomatous rosettes (ependymoblastoma) or have extensive neuronal differentiation (cerebral neuroblastoma) with ganglion cells (ganglioneuroblastoma).
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Adesina, A.M., Hunter, J., Rorke-Adams, L. (2010). Central Nervous System Primitive Neuroectodermal Tumors and Medulloepithelioma. In: Adesina, A., Tihan, T., Fuller, C., Poussaint, T. (eds) Atlas of Pediatric Brain Tumors. Springer, New York, NY. https://doi.org/10.1007/978-1-4419-1062-2_6
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DOI: https://doi.org/10.1007/978-1-4419-1062-2_6
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