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Vascular Tumors of the Lungs

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Book cover Diagnostic Pathology of Pleuropulmonary Neoplasia

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Abstract

Contrary to their counterparts in other organ systems, primary vascular neoplasms of the lung are rare. Because of the rarity of these lesions, the clinical and radiological features are often mistaken for other, more common lesions. Both benign and malignant vascular tumors have been described. Before a diagnosis of a primary malignant vascular neoplasm can be rendered, metastasis from extrapulmonary sites will have to be excluded through thorough clinical and radiological investigations. Primary vascular tumors of the lungs include hemangioma, lymphangioma, angiolymphoid hyperplasia with eosinophilia, and capillary hemangiomatosis among the benign lesions and epithelioid hemangioendothelioma, angiosarcoma, and Kaposi’s sarcoma among the malignant ones (Table 8.1).

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  1. Department of Pathology, The University of Texas MD Anderson Cancer Center, Houston, TX, USA

    Annikka Weissferdt M.D., FRCPath & Cesar A. Moran M.D.

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Weissferdt, A., Moran, C.A. (2013). Vascular Tumors of the Lungs. In: Diagnostic Pathology of Pleuropulmonary Neoplasia. Springer, New York, NY. https://doi.org/10.1007/978-1-4419-0787-5_8

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