Lymphangioleiomyomatosis

Popper, Helmut H.; Morad, Nader; Al-Bozom, Issam A.; Mujeeb, Imaad Bin; Fraire, Armando E.

doi:10.1007/978-0-387-89839-1_17

Helmut H. Popper M.D⁹,
Nader Morad M.D., Ph.D¹⁰,
Issam A. Al-Bozom M.D¹¹,
Imaad Bin Mujeeb M.D¹¹ &
…
Armando E. Fraire M.D¹²

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Abstract

A unique disorder, lymphangioleiomyomatosis (LAM) is characterized by proliferation of small myoid cells with formation of numerous cystic spaces that greatly distort the normal architecture of the lung. Currently, LAM is regarded as a member of the family of PEComas (tumors derived from perivascular epithelial cells) and is closely associated with tuberous sclerosis, multifocal micronodular pneumocyte hyperplasia, and angiomyolipomas of the kidney.

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Authors and Affiliations

University of Graz School of Medicine, Graz, Austria
Helmut H. Popper M.D
University of Massachusetts Medical School, Worcester, MA, USA
Nader Morad M.D., Ph.D
Hamad Medical Corporation, Doha, Qatar
Issam A. Al-Bozom M.D & Imaad Bin Mujeeb M.D
University of Massachusetts Medical School, Worcester, MA, USA
Armando E. Fraire M.D

Authors

Helmut H. Popper M.D
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Nader Morad M.D., Ph.D
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Issam A. Al-Bozom M.D
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Imaad Bin Mujeeb M.D
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Armando E. Fraire M.D
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Editors and Affiliations

School (UMMS), Dept. Pathology, University of Massachusetts Medical, Lake Avenue N. 55, Worcester, 01655, USA
Armando E. Fraire
Cornell University, Methodist Hospital, Weill Medical College of, Fannin St. 6565, Houston, 77030, USA
Philip T. Cagle
Medical School, University of Massachusetts, Lake Avenue North 55, Worcester, 01655-0330, USA
Richard S. Irwin
Cornell University, Methodist Hospital, Weill Medical College of, Fannin St. 6565, Houston, 77030, USA
Dina R. Mody
Beth Israel Deaconess Medical Center, Dept. Anesthesia, Harvard Medical School, Deaconess Rd. 1, Boston, 02215, USA
Armin Ernst
Methodist Hospital, Fannin St. 6550, Houston, 77030, USA
Shanda Blackmon
Health Science Center at Tyler, Dept. of Pathology, University of Texas, Highway 271 11937, Tyler, 75708-3154, USA
Timothy Craig Allen
Texas Children's Hospital, Fannin Street 6621, Houston, 77030, USA
Megan K. Dishop

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Popper, H.H., Morad, N., Al-Bozom, I.A., Mujeeb, I.B., Fraire, A.E. (2010). Lymphangioleiomyomatosis. In: Fraire, A., et al. Atlas of Neoplastic Pulmonary Disease. Springer, Boston, MA. https://doi.org/10.1007/978-0-387-89839-1_17

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DOI: https://doi.org/10.1007/978-0-387-89839-1_17
Published: 21 October 2009
Publisher Name: Springer, Boston, MA
Print ISBN: 978-0-387-89838-4
Online ISBN: 978-0-387-89839-1
eBook Packages: MedicineMedicine (R0)

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