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Thoracic Manifestations of Systemic Diseases

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Pediatric Chest Imaging

Part of the book series: Medical Radiology ((Med Radiol Diagn Imaging))

Abstract

A wide variety of systemic diseases have manifestations in the pediatric chest. Among these systemic diseases are connective tissue diseases, granulomatous diseases, immunodeficiency disorders, vasculitis, sickle cell disease, cystic fibrosis, ciliary dyskinesia, histiocytosis, phakomatoses, and storage disorders. The primary manifestations are diverse, and may include interstitial lung disease, air space disease, pleuritis, lymphadenopathy, and skeletal abnormalities. Secondary effects, such as bronchiectasis from recurrent infection, are also common. Although the underlying systemic disease has often been previously diagnosed, it is not uncommon for pulmonary manifestations to be the first signs of a systemic disease, and knowledge of the pertinent clinical and imaging features may allow the radiologist to be the first to suggest an underlying systemic disease.

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Authors and Affiliations

  1. Mallinckrodt Institute of Radiology, Washington University School of Medicine, St. Louis, MO, USA

    David V. Holland

  2. Department of Pediatric Radiology, Texas Children’s Hospital, Baylor College of Medicine, 6701 Fannin St, Suite 470, Houston, TX, 77030, USA

    R. Paul Guillerman

  3. Department of Radiology, Children’s Hospital Medical Center, Cincinnati, OH, USA

    Alan S. Brody

Authors
  1. David V. Holland
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  2. R. Paul Guillerman
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  3. Alan S. Brody
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Corresponding author

Correspondence to R. Paul Guillerman .

Editor information

Editors and Affiliations

  1. Department of Pediatric Radiology, Vall d´Hebron Children´s University Hospital, Barcelona, Spain

    Pilar Garcia-Peña

  2. Department of Pediatric Radiology, Baylor College of Medicine, Houston, Texas, USA

    R. Paul Guillerman

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© 2014 Springer-Verlag Berlin Heidelberg

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Holland, D.V., Paul Guillerman, R., Brody, A.S. (2014). Thoracic Manifestations of Systemic Diseases. In: Garcia-Peña, P., Guillerman, R. (eds) Pediatric Chest Imaging. Medical Radiology(). Springer, Berlin, Heidelberg. https://doi.org/10.1007/174_2014_965

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  • DOI: https://doi.org/10.1007/174_2014_965

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  • Print ISBN: 978-3-642-37336-7

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