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Imaging Features of Granulomatosis with Polyangiitis (Wegener’s)

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Systemic Vasculitis

Part of the book series: Medical Radiology ((Med Radiol Diagn Imaging))

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Abstract

Granulomatosis with polyangiitis or Wegener’s granulomatosis is a small-vessel vasculitis characterized by necrotizing granulomatous inflammation with involvement of: (1) Upper airways (sinusitis, otitis, ulcerations, bone deformities, subglotic or bronchial stenosis), (2) Lower respiratory tract (cough, chest pain, dyspnea, and hemoptysis), (3) Glomerulonephritis (hematuria, red blood cell casts, proteinuria, and azotemia). When Granulomatosis with polyangiitis (Wegener’s) is suspected, the search to locate involvement of the upper respiratory tract, lungs and airways, CNS, or kidneys should include: (a) A clinical ORL exam and a sinonasal CT or MRI, (b) A high resolution chest CT, (c) An electrocardiogram (ECG), (d) Research of proteinuria and urinary sediment, (e) An ophthalmological exam, (f) Titers of c-ANCA and PR3 (antiprotease 3).

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Silvera, S., Palangié, E., Guillevin, L., Hendaoui, L., Legmann, P. (2011). Imaging Features of Granulomatosis with Polyangiitis (Wegener’s). In: Hendaoui, L., Stanson, A., Bouhaouala, M., Joffre, F. (eds) Systemic Vasculitis. Medical Radiology(). Springer, Berlin, Heidelberg. https://doi.org/10.1007/174_2011_289

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