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Congenital Lobar Emphysema

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Pediatric Thoracic Surgery

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Abstract

Congenital lobar emphysema (CLE) is a pulmonary congenital malformation characterized by hyperinflation. After birth, a dysfunctional valve mechanism (air enters the alveoli thanks to negative pressure but cannot be released because the tracheobronchial tree has collapsed) leads to air trapping. CLE has all the features of obstructive emphysema: compression of lung parenchyma; mediastinal shift, herniation of the emphysematous lobe across the anterior mediastinum; and reduced respiratory reserve due to lowering of the diaphragm [1–2].

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Authors and Affiliations

  1. Pediatric Surgery, University of Bologna, Bologna, Italy

    Mario Lima

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  1. Giovanni Ruggeri
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  2. Michela Maffi
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  3. Francesca Destro
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  4. Mario Lima
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Correspondence to Mario Lima .

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  1. Pediatric Surgery, University of Bologna, Bologna, Italy

    Mario Lima

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Ruggeri, G., Maffi, M., Destro, F., Lima, M. (2013). Congenital Lobar Emphysema. In: Lima, M. (eds) Pediatric Thoracic Surgery. Springer, Milano. https://doi.org/10.1007/978-88-470-5202-4_23

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  • DOI: https://doi.org/10.1007/978-88-470-5202-4_23

  • Publisher Name: Springer, Milano

  • Print ISBN: 978-88-470-5201-7

  • Online ISBN: 978-88-470-5202-4

  • eBook Packages: MedicineMedicine (R0)

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