, Volume 9, Issue 2, pp 246-249
Date: 13 Mar 2013

Perianal alveolar soft-part sarcoma: a rare case

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Abstract

Background

Alveolar soft part sarcoma (ASPS) is a rare diagnosis in the perianal region.

Methods

we describe the clinical presentation, pathological findings and differential diagnosis of a rare case of perianal ASPS. We also describe the importance of the preoperative embolization of the hypervascularised masses to prevent surgical bleeding.

Conclusions

clinical and pathological findings are essential for the diagnosis, specifically by immunochemistry and molecular techniques, as the demonstration of ASPL/TFE3 fusion transcript became indispensable in some cases. Preoperative embolization of the hypervascularised masses may prevent uncontrollable surgical bleeding.