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Thrombotic thrombocytopenic purpura in a new onset lupus patient?

  • Novel Aspects in Lupus, 2017
  • Published:
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Abstract

We are presenting a case of TTP with undetectable levels of ADAMTS 13 in a 39-year-old woman. Diagnosis of systemic lupus was evoked in the setting of thrombotic microangiopathy. The patient presented normal renal function but important neurological impairment. Treatment with daily plasmapheresis as well as Rituximab, cyclophosphamide as steroids was required to achieve clinical improvement.

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Authors and Affiliations

  1. Hospital Universitario de Gran Canaria Dr Negrin, Las Palmas, Spain

    Nery Sablón González, Yanet Parodis, Maria Belen Alonso Ortiz & Jose Carlos Rodriguez Perez

  2. Centre Hospitalier Saint Cyr, Lyon, France

    Noel Lorenzo

  3. Hopital Universitaire Fattouma Bourguiba, Monastir, Tunisia

    Melek Kechida

Authors
  1. Nery Sablón González
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  2. Noel Lorenzo
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  3. Yanet Parodis
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  4. Maria Belen Alonso Ortiz
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  5. Melek Kechida
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  6. Jose Carlos Rodriguez Perez
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Corresponding author

Correspondence to Noel Lorenzo.

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González, N.S., Lorenzo, N., Parodis, Y. et al. Thrombotic thrombocytopenic purpura in a new onset lupus patient?. Immunol Res 65, 454–458 (2017). https://doi.org/10.1007/s12026-017-8898-y

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  • DOI: https://doi.org/10.1007/s12026-017-8898-y

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