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Marfan syndrome presenting with abdominal aortic aneurysm during pregnancy

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Summary

Methods

We report a case of successfully performed Caesarean section followed by reconstruction of the abdominal aorta in a patient with Marfan syndrome.

Results

A 35-year-old woman at 37 weeks’ gestation in her second pregnancy was referred with abdominal aortic aneurysm. On admission she was asymptomatic, haemodynamically stable, and without clinical and radiological signs of rupture. Magnetic resonance imaging confirmed that the infrarenal aortic aneurysm continued to the right common iliac artery. Following preoperative assessment, it was decided to finalize gestation and reconstruct the aorta in a one-stage procedure. After a median xyphopubic laparotomy, Mizgav–Ladach Caesarean section and Pomeroy tubal sterilization were performed, followed by aneurysmectomy and aorto-bilateral iliac artery bypass. The postoperative course was uneventful. Both mother and child were doing well at follow-up 3, 9 and 12 months after the intervention.

Conclusion

To the best of our knowledge, this is the first case of true abdominal aortic aneurysm repair and Caesarean section as a one-stage procedure.

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Authors and Affiliations

  1. Department of Surgery, Faculty of Medicine, University of Novi Sad, Novi Sad, Serbia

    J. Pasternak MD, Ph.D & N. Budakov MD

  2. Department for Vascular Surgey, Clinical Centre Vojvodine, Hajduk Veljkova 1, 21000, Novi Sad, Serbia

    J. Pasternak MD, Ph.D, M. Kaćanski MD & N. Budakov MD

Authors
  1. J. Pasternak MD, Ph.D
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  2. M. Kaćanski MD
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  3. N. Budakov MD
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Corresponding author

Correspondence to J. Pasternak MD, Ph.D.

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Conflict of interest

J. Pasternak, M. Kaćanski and N.J. Budakov declare that they have no competing interests.

Ethical standards

All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional and/or national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards. Informed consent was obtained from all individual participants included in the study.

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Pasternak, J., Kaćanski, M. & Budakov, N. Marfan syndrome presenting with abdominal aortic aneurysm during pregnancy. Eur Surg 49, 38–40 (2017). https://doi.org/10.1007/s10353-016-0456-7

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  • DOI: https://doi.org/10.1007/s10353-016-0456-7

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