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Osteopathia striata with cranial sclerosis (OSCS): review of the literature and case report demonstrating challenges of spinal fusion after trauma

  • Case Report - Spine
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Abstract

Osteopathia striata with cranial sclerosis (OSCS) is a rare but well-described pathology characterized by abnormalities in bone deposition in the axial and cranial skeleton as well as other abnormalities and associated deficits. These skeletal abnormalities can lead to significant intra-operative challenges for the surgeon and influence outcomes for the patient. In this report, we present a case of a patient with OSCS who was involved in a traumatic motor vehicle crash and underwent posterior cervico-thoracic fusion for a T4 chance fracture. Bony abnormalities in the cervico-thoracic spine presented a significant operative challenge due to alterations in bony anatomy and bone architecture. This case serves as an example of the challenges that the spine surgeon faces when dealing with OSCS, and highlights the differences between OSCS and commoner skeletal hyperplasias such as osteopetrosis.

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Acknowledgments

An American Medical Association Seed Grant, a Neurosurgery Research and Education Foundation Medical Student Summer Fellowship, a Sigma Xi Grants in Aid of Research, and American Foundation of Pharmaceutical Education Pre-doctoral Fellowship supported Brandon Lucke-Wold.

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Authors and Affiliations

  1. Department of Neurosurgery, West Virginia University School of Medicine, One Medical Center Drive Suite 4300, Morgantown, WV, 26506, USA

    Gennadiy A. Katsevman, Ryan C. Turner, Brandon P. Lucke-Wold, Cara L. Sedney & Sanjay Bhatia

  2. Center for Neuroscience, West Virginia University School of Medicine, Morgantown, WV, 26506, USA

    Gennadiy A. Katsevman, Ryan C. Turner, Brandon P. Lucke-Wold, Cara L. Sedney & Sanjay Bhatia

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  1. Gennadiy A. Katsevman
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  2. Ryan C. Turner
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  3. Brandon P. Lucke-Wold
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  4. Cara L. Sedney
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  5. Sanjay Bhatia
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Corresponding author

Correspondence to Sanjay Bhatia.

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The patient and patient’s mother has consented to submission of this case report to the journal.

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The author(s) declare that they have no competing interests.

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Katsevman, G.A., Turner, R.C., Lucke-Wold, B.P. et al. Osteopathia striata with cranial sclerosis (OSCS): review of the literature and case report demonstrating challenges of spinal fusion after trauma. Acta Neurochir 158, 1115–1120 (2016). https://doi.org/10.1007/s00701-016-2794-4

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  • DOI: https://doi.org/10.1007/s00701-016-2794-4

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