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Emergency bronchoscopy for foreign-body aspiration in a child with type I mucopolysaccharidosis: a challenging airway management experience

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Abstract

The mucopolysaccharidosis (MPS) is a rare lysosomal storage disease. Glycosaminoglycans (GAG) accumulate in musculoskeletal system, connective tissues. Enlarged tongue, short immobile neck, and limited mobility of the cervical spine and temporomandibular joints render the airway management potentially risky. MPS children have high anesthetic risks, especially in airway management of emergency situations. The foreign-body aspiration requiring intervention with rigid bronchoscopy is an urgent and risky clinical situation. We present our experience with a challenging airway management with a three-year-old child with MPS who needed emergency bronchoscopy due to peanut aspiration.

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Authors and Affiliations

  1. Department of Anesthesiology and Intensive Care, Cerrahpasa Medical Faculty, Istanbul University, Kocamustafapasa, Fatih, 34098, Istanbul, Turkey

    Pinar Kendigelen, Yusuf Tunali, Ayse Tutuncu, Gulruh Ashyralyyeva & Guner Kaya

  2. Department of Pediatric Surgery, Cerrahpasa Medical Faculty, Istanbul University, Istanbul, Turkey

    Senol Emre

Authors
  1. Pinar Kendigelen
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  2. Yusuf Tunali
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  3. Ayse Tutuncu
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  4. Gulruh Ashyralyyeva
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  5. Senol Emre
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  6. Guner Kaya
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Corresponding author

Correspondence to Pinar Kendigelen.

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The authors report no conflicts of interest.

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Written informed consent was obtained from the parent.

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Cite this article

Kendigelen, P., Tunali, Y., Tutuncu, A. et al. Emergency bronchoscopy for foreign-body aspiration in a child with type I mucopolysaccharidosis: a challenging airway management experience. J Anesth 30, 696–698 (2016). https://doi.org/10.1007/s00540-016-2180-7

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  • DOI: https://doi.org/10.1007/s00540-016-2180-7

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